Maxillary sinus augmentation in a patient with hereditary angioedema with normal C1 inhibitor and familial Mediterranean fever

IF 0.4 Q4 DENTISTRY, ORAL SURGERY & MEDICINE
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引用次数: 0

Abstract

Hereditary angioedema (HAE) with normal C1 inhibitor (C1-INH) (HAE-nC1-INH) is a rare disease that presents with laryngeal edema due to oral surgical procedures. Familial Mediterranean fever (FMF) is a disorder commonly characterized by an autosomal recessive inflammatory process, and manifests in the oral cavity and facial structures. A 50-year-old woman with HAE-nC1-INH and FMF was referred to our department for bone augmentation in the right maxillary molar region. We performed lateral window sinus augmentation under the backup support of an anesthesiologist. A hematologist used intravenous Berinert® and oral Orladeyo® to prevent perioperative angioedema attacks. The postoperative course was uneventful. Regarding surgical intervention in patients with HAE, interdepartmental cooperation is crucial to prevent angioedema attacks and prepare for life-threatening complications. Oral hygiene and occlusion should be considered in the dental implant treatment of patients with FMF. Every oral and maxillofacial surgeon and dental practitioner should familiarize themselves with HAE and FMF.

一名 C1 抑制剂正常的遗传性血管性水肿和家族性地中海热患者的上颌窦扩张术
伴有正常 C1 抑制剂(C1-INH)的遗传性血管性水肿(HAE)(HAE-nC1-INH)是一种罕见疾病,会因口腔外科手术而出现喉头水肿。家族性地中海热(FMF)是一种以常染色体隐性遗传炎症过程为常见特征的疾病,表现为口腔和面部结构。一名患有 HAE-nC1-INH 和 FMF 的 50 岁女性因右侧上颌臼齿区骨增量术转诊至我科。我们在麻醉师的后备支持下进行了侧窗鼻窦增量术。血液科医生使用静脉注射贝林特®和口服奥拉迪约®来预防围手术期血管性水肿发作。术后恢复顺利。关于HAE患者的手术治疗,跨部门合作对于预防血管性水肿发作和应对危及生命的并发症至关重要。在对 FMF 患者进行种植牙治疗时,应考虑口腔卫生和咬合问题。每一位口腔颌面外科医生和牙科医生都应熟悉 HAE 和 FMF。
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来源期刊
CiteScore
0.80
自引率
0.00%
发文量
129
审稿时长
83 days
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