Beware of the Coated Aorta in Fluorodeoxyglucose Positron Emission Tomography-Computed Tomography: A Specific Clue to the Diagnosis of Erdheim-Chester Disease in a Case of Brain and Orbital Lesions with Unknown Primary.

IF 0.4 Q4 RADIOLOGY, NUCLEAR MEDICINE & MEDICAL IMAGING
Indian Journal of Nuclear Medicine Pub Date : 2023-10-01 Epub Date: 2023-12-20 DOI:10.4103/ijnm.ijnm_63_23
Koramadai Karuppusamy Kamaleshwaran, Elumalai Ramkumar
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引用次数: 0

Abstract

Erdheim-Chester disease (ECD) is a systemic histiocytosis that can involve several organs, with severity ranging from occult to life-threatening. The disease was first described by William Chester in 1930 after working with the Austrian pathologist Jakob Erdheim. Even today, a correct diagnosis of ECD often takes years, given the rarity and variable manifestations of ECD. We present a case of a 63-year-old female presenting with multiple brain lesions, sent for fluorine-18 fluorodeoxyglucose positron emission tomography/computed tomography to find primary, and it showed hypermetabolic right occipital brain lesion, right orbital lesion, and soft tissue around the arch of the aorta (coated aorta), and final histopathology of the brain lesion confirmed histiocytosis ECD.

当心氟脱氧葡萄糖正电子发射断层扫描-计算机断层扫描中的涂层主动脉:在一例原发性不明的脑部和眼眶病变中诊断埃尔德海姆-切斯特病的特异线索。
埃尔德海姆-切斯特病(Erdheim-Chester disease,ECD)是一种全身性组织细胞增生症,可累及多个器官,严重程度从隐匿性到危及生命不等。威廉-切斯特与奥地利病理学家雅各布-埃尔德海姆(Jakob Erdheim)合作后,于 1930 年首次描述了这种疾病。即使在今天,由于 ECD 的罕见性和多变表现,正确诊断 ECD 也往往需要数年时间。我们介绍了一例 63 岁女性的病例,她出现多发性脑部病变,送去进行氟-18 氟脱氧葡萄糖正电子发射断层扫描/计算机断层扫描以寻找原发病灶,结果显示右枕部脑部病变、右眼眶病变和主动脉弓周围软组织(涂层主动脉)均呈高代谢性,最终脑部病变组织病理学证实为组织细胞增生症 ECD。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
Indian Journal of Nuclear Medicine
Indian Journal of Nuclear Medicine RADIOLOGY, NUCLEAR MEDICINE & MEDICAL IMAGING-
CiteScore
0.70
自引率
0.00%
发文量
46
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