Left Isomerism (Polysplenia Syndrome)

Q4 Medicine
Mircea Stoian, Radu Ionescu
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引用次数: 0

Abstract

Left isomerism (IS), also known as polysplenic syndrome, is part of the category of heterotaxic syndromes. Heterotaxic syndrome is a general term that describes the abnormal positioning of the viscera in the chest and abdomen. Signs of polysplenic syndrome include: bilobed lungs, liver located on the median line, but also intestinal malrotation. The prevalence of this condition is 1.4 patients per 10,000 children. The clinical aspect is closely correlated with the specific pathology of polysplenism. Apparently, incidental signs and symptoms are encountered, unexplained and unassociated from the etiopathogenic point of view, until the imaging examination that elucidates the causes of the observed clinical picture. As such, polysplenism, i.e., left isomerism, is the result of the abnormal development of the asymmetry of the laterality of the organs having the effect of situs ambiguus.
左同分异构体(多脾综合征)
左同分异构体(IS),又称多脾综合征,是异位综合征的一部分。异位综合征是指脏器在胸腹位置异常的总称。多脾综合征的征象包括:双叶肺,肝位于中线,但也有肠旋转不良。这种疾病的患病率为每10,000名儿童中有1.4名患者。多性症的临床表现与多性症的具体病理密切相关。显然,偶发的体征和症状是无法解释的,从致病的角度来看是无关的,直到影像学检查阐明了所观察到的临床症状的原因。因此,多性体,即左同分异构体,是器官侧偏不对称发育异常的结果,具有歧义位置的影响。
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来源期刊
Surgery, Gastroenterology and Oncology
Surgery, Gastroenterology and Oncology Medicine-Gastroenterology
CiteScore
0.30
自引率
0.00%
发文量
11
期刊介绍: Starting with this issue "Annals of Fundeni Hospital", founded in 1996 as the scientific journal of the prestigious hospital Fundeni becomes "Journal of Translational Medicine and Research" (JTMR), an Journal of the Academy of Medical Sciences of Romania. Therefore, an 18 years old Journal, attested and indexed in Elsevier Bibliographic Databases, Amsterdam and also indexed in SCOPUS, is continuing a tradition of excellence that lasted almost two decades. The new title of the Journal is inspired first of all from the important developments of translational research In Fundeni Clinical Institute and the "C.C Iliescu Institute for Cardio-Vascular Diseases", in parallel with the national and international trend to promote and develop this important area or medical research. Although devoted mainly to translational research, JTMR will continue to promote both basic and clinical research.
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