Spinocerebellar Degeneration (SCD)

Abstract

Spinocerebellar degeneration (SCD) is a group of neurodegenerative disorders characterized by progressive cerebellar ataxia with or without symptoms/signs of pyramidal, extrapyramidal, or peripheral nerve involvement. Patients frequently exhibit unsteadiness of gait associated with nystagmus, which could also be observed in patients with peripheral vestibular impairment. Thus, some of these patients often initially seek consultation with an otolaryngologist. To distinguish SCD from other peripheral vestibular disorders, it is necessary for otolaryngologists to understand the characteristics of SCD.