Inflammatory Pseudotumor-Like Follicular/Fibroblastic Dendritic Cell Sarcoma: Focus on Surgical Treatment Approach

IF 16.4 1区化学 Q1 CHEMISTRY, MULTIDISCIPLINARY

Accounts of Chemical Research Pub Date : 2023-02-28 DOI:10.33425/2689-1093.1050

Zarrin Hossein-zadeh, Katherine Rivero-Soto, Roberto Rivero-Soto

引用次数: 0

Abstract

Inflammatory pseudotumor-like follicular/fibroblastic dendritic cell sarcoma (IPT-like FDC sarcomas, also known as FDC/FRC sarcoma) is a subgroup of follicular dendritic cell sarcoma (FDC), a rare neoplasm that often occurs in the spleen [1]. FDC/FRC sarcomas can affect other organs including the liver, colon, and the peripancreatic region [2-4]. The tumor has a predilection for young to middle-aged adults and may present with subset of symptoms including fever, abdominal pain, sweats, fatigue, and commonly a splenic solitary mass formation [5]. FDC/FRC sarcoma comprises of neoplastic spindle cells, typically with a follicular dendritic cell differentiation and over 90% of the cases are associated with EBV infection [6]. Here we present the a case of a IPT-like FDC sarcoma in a 49- year old female treated with splenectomy and a review of the literature.

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炎性假肿瘤样滤泡/成纤维树突状细胞肉瘤:手术治疗方法的重点

炎性假肿瘤样滤泡/成纤维树突状细胞肉瘤(IPT-like FDC sarcoma，又称FDC/FRC sarcoma)是滤泡树突状细胞肉瘤(follicular dendritic cell sarcoma, FDC)的一个亚群，是一种常见于脾脏的罕见肿瘤[1]。FDC/FRC肉瘤可累及肝脏、结肠和胰周等其他器官[2-4]。该肿瘤易发于青年至中年人，可出现发热、腹痛、出汗、疲劳等症状，通常为脾脏孤立性肿块形成[5]。FDC/FRC肉瘤由肿瘤梭形细胞组成，通常伴有滤泡树突状细胞分化，90%以上的病例与EBV感染有关[6]。在此，我们报告一位49岁女性，以脾切除术治疗ipt样FDC肉瘤，并回顾相关文献。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Accounts of Chemical Research 化学-化学综合

CiteScore

31.40

自引率

1.10%

发文量

312

审稿时长

2 months

期刊介绍： Accounts of Chemical Research presents short, concise and critical articles offering easy-to-read overviews of basic research and applications in all areas of chemistry and biochemistry. These short reviews focus on research from the author’s own laboratory and are designed to teach the reader about a research project. In addition, Accounts of Chemical Research publishes commentaries that give an informed opinion on a current research problem. Special Issues online are devoted to a single topic of unusual activity and significance. Accounts of Chemical Research replaces the traditional article abstract with an article "Conspectus." These entries synopsize the research affording the reader a closer look at the content and significance of an article. Through this provision of a more detailed description of the article contents, the Conspectus enhances the article's discoverability by search engines and the exposure for the research.