Dyke-Davidoff-Masson Syndrome: A Case Report and Review of Literature

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological disorder caused by brain injury in intrauterine or early years of life. Characteristic findings are prominent cortical sulci, dilated lateral ventricles, cerebral hemiatrophy, hyperpneumatization of the frontal sinus and compensatory hypertrophy of the skull. Hereby describing a male patient who presented with generalized tonic-clonic seizure and left-sided body weakness with neuroimaging findings of cerebral hemiatrophy, right lateral ventricle dilatation, hyperpneumatization of right frontal sinus, and asymmetric calvarial thickening. The above mentioned imaging features enables timely and accurate diagnosis, allowing appropriate management.