SURGICAL TREATMENT OF COMPLEX CROUZON SYNDROME CRANIOSYNOSTOSIS

Abstract

Crouzon syndrome is one of the most common syndromic craniosynostosis. We present complex course of treatment in a child with Crouzon syndrome presented with multisuture craniosynostosis and hydrocephalus. A 3-months-old boy was admitted with clinical signs of hydrocephalus and turribrachycephaly. Firstly, the hydrocephalus was addressed. The ventriculoperitoneal shunt with programmable valve was implanted. Secondly, in May 2017, posterior calvarial remodeling was done. Finally, after the child recovered, anterior calvarial remodeling with fronto-orbital advancement was performed.  This completed the calvarial remodeling in this patient. Child is doing well, so far completing milestones of child development in time. This case presents an extremely complex case of syndromic multisuture craniosynostosis, in which it was necessary to perform the entire calvarial remodeling to correct the deformity and to provide a chance to the brain to grow and develop without constrictions.