IgG4 Cholangitis Simulating Cholangiocarcinoma: A Diagnostic Trap

Abstract

IgG4‐related sclerosing cholangitis (IgG4‐SC) is the biliary manifestation of IgG4‐related disease, systemic fibroinflammatory condition that is characterized by lesions with classical histopathological findings in involved organs. We presented a case of isolated IgG4‐SC with the normal serum IgG4 which was hard to differentiate with cholangiocarcinoma.