Renal cell carcinoma arising within autosomal dominant polycystic kidney disease

Abstract

Renal cell carcinoma (RCC) arising within autosomal dominant polycystic kidney disease (ADPKD) is rare. The detection of this complication in patients with ADPKD is difficult owing to the nonspecific symptoms. Here, we describe a case of a young woman who presented with RCC in the background of ADPKD. She had radical nephrectomy, followed by adjuvant chemotherapy.