儿童下颌骨纤维瘤病——根治性治疗是否合理?

National Journal of Maxillofacial Surgery Pub Date : 2023-01-01 Epub Date: 2023-04-14 DOI:10.4103/njms.njms_71_22
Manish J Raghani, Subham S Agarwal, Hafiz M N Ansari
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引用次数: 0

摘要

婴儿纤维瘤病的特点是纤维软组织增生,有可能侵犯邻近结构,但缺乏转移能力,因此是一种具有边界特征的相当良性的病变。病理学类似于肉瘤的生长,因此临床医生很难正确诊断。根据其主要涉及的年龄组,有两种变体,即青少年和成人的腹外硬纤维变体。纤维瘤病是一种相对罕见的肿瘤,具有不可预测的生长和不同的局部复发率。肿块通常生长缓慢,生长迅速,复发主要与幼年型有关。该疾病可能表现为分布广泛的单灶或多灶病变,因此需要全身扫描来识别其他地方的任何潜在生长。在此,我们报告一例2岁儿童复发性青少年/婴儿纤维瘤病,保守治疗,无任何生长障碍和复发迹象。
本文章由计算机程序翻译,如有差异,请以英文原文为准。

Infantile fibromatosis of the mandible- Is radical treatment justified?

Infantile fibromatosis of the mandible- Is radical treatment justified?

Infantile fibromatosis of the mandible- Is radical treatment justified?

Infantile fibromatosis of the mandible- Is radical treatment justified?

Infantile fibromatosis is characterized by proliferation of fibrous soft tissue with a potential of invading the adjacent structures but lacks the ability to metastasize, thus making it a fairly benign lesion with borderline characteristics. The pathology resembles sarcomatous growth, therefore making it difficult for the clinician to correctly diagnose. There are two variants of extra-abdominal desmoid juvenile and adult variant depending upon the age group it predominately involves. Fibromatosis is comparatively a rare tumour with unpredictable growth and varying local recurrence rates. The mass usually grows slowly, rapid growth and recurrences being mostly associated with the juvenile forms. The disease may present as single or multifocal lesion with widespread distribution, thus requiring whole body scans to identify any insidious growth elsewhere. Here, we report a case of recurrent juvenile/infantile fibromatosis in a 2-year-old child, conservatively managed without any growth disturbance and signs of recurrence.

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