{"title":"心律失常性右心室发育不良,我们知道一切吗?收到更新","authors":"A. Kinsara","doi":"10.17554/j.issn.2309-6861.2018.05.160","DOIUrl":null,"url":null,"abstract":"Arrhythmogenic right ventricular dysplasia is a cardiomyopathy of the young that presents with a sudden cardiac death. It has unique features that prompted a different classification, based on a combination of right ventricular imaging by echocardiography and cardiac magnetic resonance imaging, histology, repolarization abnormalities, depolarization and conduction abnormalities, arrhythmias and family history (including genetic testing). Hence the usual investigative pathway requires a multimodality approach. Treatment is complex and starts with exercise restriction in this young active population and ends up with insertion of an Automated ORIGINAL ARTICLE Arrhythmogenic Right Ventricular Dysplasia, Did We Know Everything Abdulhalim Jamal Kinsara, FRCP 747 Journal of Cardiol Ther 2018 October; 5(1): 747-750 ISSN 2309-6861(print), ISSN 2312-122X(online) Online Submissions: http: //www.ghrnet.org/index./jct/ doi: 10.17554/j.issn.2309-6861.2018.05.160 Journal of Cardiology and Therapy truncation. However, the presence of desmosomal mutations did not affect the prognosis[9].","PeriodicalId":92802,"journal":{"name":"Journal of clinical cardiology and cardiovascular therapy","volume":"23 1","pages":"747-750"},"PeriodicalIF":0.0000,"publicationDate":"2018-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Arrhythmogenic Right Ventricular Dysplasia, Did We KnowEverything: Kinsara AJ et al. ARVD update\",\"authors\":\"A. Kinsara\",\"doi\":\"10.17554/j.issn.2309-6861.2018.05.160\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Arrhythmogenic right ventricular dysplasia is a cardiomyopathy of the young that presents with a sudden cardiac death. It has unique features that prompted a different classification, based on a combination of right ventricular imaging by echocardiography and cardiac magnetic resonance imaging, histology, repolarization abnormalities, depolarization and conduction abnormalities, arrhythmias and family history (including genetic testing). Hence the usual investigative pathway requires a multimodality approach. Treatment is complex and starts with exercise restriction in this young active population and ends up with insertion of an Automated ORIGINAL ARTICLE Arrhythmogenic Right Ventricular Dysplasia, Did We Know Everything Abdulhalim Jamal Kinsara, FRCP 747 Journal of Cardiol Ther 2018 October; 5(1): 747-750 ISSN 2309-6861(print), ISSN 2312-122X(online) Online Submissions: http: //www.ghrnet.org/index./jct/ doi: 10.17554/j.issn.2309-6861.2018.05.160 Journal of Cardiology and Therapy truncation. However, the presence of desmosomal mutations did not affect the prognosis[9].\",\"PeriodicalId\":92802,\"journal\":{\"name\":\"Journal of clinical cardiology and cardiovascular therapy\",\"volume\":\"23 1\",\"pages\":\"747-750\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2018-01-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Journal of clinical cardiology and cardiovascular therapy\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.17554/j.issn.2309-6861.2018.05.160\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Journal of clinical cardiology and cardiovascular therapy","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.17554/j.issn.2309-6861.2018.05.160","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Arrhythmogenic Right Ventricular Dysplasia, Did We KnowEverything: Kinsara AJ et al. ARVD update
Arrhythmogenic right ventricular dysplasia is a cardiomyopathy of the young that presents with a sudden cardiac death. It has unique features that prompted a different classification, based on a combination of right ventricular imaging by echocardiography and cardiac magnetic resonance imaging, histology, repolarization abnormalities, depolarization and conduction abnormalities, arrhythmias and family history (including genetic testing). Hence the usual investigative pathway requires a multimodality approach. Treatment is complex and starts with exercise restriction in this young active population and ends up with insertion of an Automated ORIGINAL ARTICLE Arrhythmogenic Right Ventricular Dysplasia, Did We Know Everything Abdulhalim Jamal Kinsara, FRCP 747 Journal of Cardiol Ther 2018 October; 5(1): 747-750 ISSN 2309-6861(print), ISSN 2312-122X(online) Online Submissions: http: //www.ghrnet.org/index./jct/ doi: 10.17554/j.issn.2309-6861.2018.05.160 Journal of Cardiology and Therapy truncation. However, the presence of desmosomal mutations did not affect the prognosis[9].