Klippel–Trenaunay Syndrome Associated with Abdominal Aortic Aneurysm

The Klippel–Trenaunay syndrome is a rare disorder characterised by well-described bony and vascular (venous and lymphatic) anomalies. Its association with arterial aneurysms has only been reported in a dozen cases, in particular, in cerebral, renal and popliteal arteries. We report the case of a 35-year-old male patient, who presented with an 85-mm aorto-iliac aneurysm primarily suspected to be mycotic, in addition to a typical single lower extremity arteriomegaly. The patient was successfully treated by means of an allograft. This is considered to be the first reported case of Klippel–Trenaunay syndrome, associated with an aortic aneurysm.