Giant Right Atrium or Ebstein Anomaly

Many acquired and congenital pathologies could cause enlargement of Right Atrium (RA). In rare pathologies we couldn’t find an obvious reason for enlargement of RA. Sometimes it leads to misdiagnosis if we try to explain an unknown pathology with well known pathology. In this article we describe a woman who presented with giant enlargement of the RA misdiagnosed as Ebstein anomaly. Cardiac MRI is highly helpful for differential diagnosis of these kinds of atrial pathologies. Although it is rare, giant RA should be considered in differential diagnosis of huge RA without an obvious cause.