{"title":"8岁女童先天性单侧上下颌骨融合1例","authors":"Satoko Koeda, Takahiro Suzuki, Hitoshi Nei, Hanae Inahara, Yoko Takata, Satoshi Goto, Hiroshi Nagasaka, Hiroshi Kawamura","doi":"10.1016/j.ajoms.2010.06.003","DOIUrl":null,"url":null,"abstract":"<div><p>Congenital fusion of the mandible to maxilla can involve soft tissue (synechiae) or bone (syngnathia). Congenital synechiae has been widely reported, whereas congenital syngnathia is rare. Syngnathia severely limits mouth opening. To improve airway control and prevent feeding handicaps, surgical division of the bony fusion or breakdown of the adhesions is recommended within the first few days of life. We described an 8-year-old girl who had unilateral syngnathia with micromandible, reactive coronoid process hyperplasia, cleft palate and congenital corneal opacity. She first underwent surgical treatment to improve jaw function at the age of 8 years. Delayed surgery slightly improved restricted mouth opening.</p></div>","PeriodicalId":100128,"journal":{"name":"Asian Journal of Oral and Maxillofacial Surgery","volume":"22 4","pages":"Pages 220-224"},"PeriodicalIF":0.0000,"publicationDate":"2010-10-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1016/j.ajoms.2010.06.003","citationCount":"4","resultStr":"{\"title\":\"A case of congenital unilateral maxillo-mandibular bony fusion in an 8-year-old girl\",\"authors\":\"Satoko Koeda, Takahiro Suzuki, Hitoshi Nei, Hanae Inahara, Yoko Takata, Satoshi Goto, Hiroshi Nagasaka, Hiroshi Kawamura\",\"doi\":\"10.1016/j.ajoms.2010.06.003\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<div><p>Congenital fusion of the mandible to maxilla can involve soft tissue (synechiae) or bone (syngnathia). Congenital synechiae has been widely reported, whereas congenital syngnathia is rare. Syngnathia severely limits mouth opening. To improve airway control and prevent feeding handicaps, surgical division of the bony fusion or breakdown of the adhesions is recommended within the first few days of life. We described an 8-year-old girl who had unilateral syngnathia with micromandible, reactive coronoid process hyperplasia, cleft palate and congenital corneal opacity. She first underwent surgical treatment to improve jaw function at the age of 8 years. Delayed surgery slightly improved restricted mouth opening.</p></div>\",\"PeriodicalId\":100128,\"journal\":{\"name\":\"Asian Journal of Oral and Maxillofacial Surgery\",\"volume\":\"22 4\",\"pages\":\"Pages 220-224\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2010-10-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://sci-hub-pdf.com/10.1016/j.ajoms.2010.06.003\",\"citationCount\":\"4\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Asian Journal of Oral and Maxillofacial Surgery\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://www.sciencedirect.com/science/article/pii/S0915699210000932\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Asian Journal of Oral and Maxillofacial Surgery","FirstCategoryId":"1085","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S0915699210000932","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
A case of congenital unilateral maxillo-mandibular bony fusion in an 8-year-old girl
Congenital fusion of the mandible to maxilla can involve soft tissue (synechiae) or bone (syngnathia). Congenital synechiae has been widely reported, whereas congenital syngnathia is rare. Syngnathia severely limits mouth opening. To improve airway control and prevent feeding handicaps, surgical division of the bony fusion or breakdown of the adhesions is recommended within the first few days of life. We described an 8-year-old girl who had unilateral syngnathia with micromandible, reactive coronoid process hyperplasia, cleft palate and congenital corneal opacity. She first underwent surgical treatment to improve jaw function at the age of 8 years. Delayed surgery slightly improved restricted mouth opening.