Melkersson-Rosenthal综合征:一个经典病例报告

C. Domaneschi, C. Arruda, V. G. Carvalho, Rennan Luiz Oliveira Dos Santos, N. Sugaya
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引用次数: 0

摘要

Melkersson-Rosenthal综合征是一种罕见的表现,其特征是三种体征和症状:复发性口面部水肿,舌裂和复发性面瘫。Melkersson-Rosenthal综合征的诊断困难在于,除了卫生专业人员对该综合征缺乏认识以及其症状经常同时表现外,口面部水肿是各种疾病的常见症状。本报告的目的是提出Melkersson-Rosenthal综合征的经典病例及其临床和治疗方法。一位到口腔诊所求诊的患者同时表现为三联征:左唇和面颊无凹陷性水肿,同时伴有同侧面瘫和舌裂。Melkersson-Rosenthal综合征的诊断是由于出现了三联征和症状,而由于缺乏肠道或呼吸系统的主诉和缺乏其他临床证据,最初排除了克罗恩病、结节病和结核病。治疗方法是类固醇,这是我们在文献中发现的梅尔克森-罗森塔尔综合征患者预后满意的最常见治疗方法。我们推荐局部注射二丙酸倍他米松,因为在四次浸润后,水肿消退了80%,在一年的随访中没有进一步复发。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Melkersson-Rosenthal syndrome: a classical case report
ABSTRACT The Melkersson-Rosenthal syndrome constitutes a rare manifestation characterized by a triad of signs and symptoms: recurrent orofacial edema, fissured tongue, and recurrent facial paralysis. The difficulty in diagnosing Melkersson-Rosenthal syndrome is that orofacial edema is common to various diseases besides the lack of awareness of the syndrome by health professionals and the frequent metachronous manifestation of its symptomatology. The aim of this report is to present a classical case of Melkersson-Rosenthal syndrome and its clinical and therapeutic approach. A patient who sought for assistance at the Stomatology Clinic presented a synchronous manifestation of the triad: a left lip and cheek nonpitting edema accompanied by facial paralysis on the same side and fissured tongue. Melkersson-Rosenthal syndrome was diagnosed due to the presence of the triad of signs and symptoms after initially ruling out Crohn’s disease, Sarcoidosis, and tuberculosis due to a lack of intestinal or respiratory complaints and absence of other clinical evidence. The treatment administered was steroids, the most common treatment with a satisfied prognosis we found in the literature for Melkersson-Rosenthal syndrome patients. We recommend its implementation intralesional injections of betamethasone dipropionate as after four infiltrations the edema subsided by 80% with no further relapses within one-year follow-up.
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