超声引导锁骨上阻滞治疗波兰综合征:全身麻醉的安全选择

V. Asthana
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引用次数: 0

摘要

波兰综合征是一种罕见的先天性异常,其特征是多系统和器官受累,如肌肉骨骼、肺、心脏、肾脏和造血系统,但没有功能残疾。右侧胸畸形是该综合征最常见的特征,缺乏底层骨骼和肌肉,使其类似于开胸以及同侧手畸形,如短指、并指或外指[1]。该综合征的发病率为每3万至5万活产1例[2]。波兰综合征患者在手术过程中需要麻醉来纠正相关的畸形或与疾病过程相关的器官系统。文献显示,这些患者在全身麻醉下,由于相关的肌肉骨骼异常,可能更容易发生恶性高热[3]。此外,围手术期的呼吸问题和缺氧可能与休息时无症状患者的呼吸异常、肺发育不全和胸壁异常有关。我们报告一例波兰综合征诊断为并拢释放提出关键词:USG阻滞,锁骨上入路。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Ultrasound Guided Supraclavicular Block in Poland Syndrome : A Safe Alternative to General Anaesthesia
Poland syndrome is an uncommon, congenital anomaly characterized by multiple systems and organs involvement like musculoskeletal, lungs, heart, kidneys and haemopoetic system with absence of functional disability. Right sided Thorax deformity is the most common feature of this syndrome with the absence of underlying bones and muscles making this condition similar to open chest along with ipsilateral hand anomalies such as brachydactyly, syndactyly or ectodactyly [1]. The incidence of this syndrome is 1 per 30,000-50,000 live births [2]. Patients with Poland syndrome require anesthesia during surgical procedures to correct the associated deformities or the organ systems associated with the disease process. Literature shows that these patients may be more susceptible for malignant hyperthermia due to associated musculoskeletal abnormalities under general anesthesia [3]. Moreover respiratory problems and hypoxia in the perioperative period may be related to associated paradoxical breathing, lung hypoplasia and chest wall abnormalities in otherwise asymptomatic patient at rest. We report a diagnosed case of Poland syndrome presented for syndactly release Keywords: USG blocks, Supraclavicular approach.
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