过早得肾透明细胞肉瘤?一个病例报告,回顾不同的考虑

IF 0.1 Q4 PATHOLOGY
D. Russell
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引用次数: 0

摘要

肾透明细胞肉瘤(CCSK)占所有儿童肾癌的3%。准确的诊断对于适当的治疗至关重要,这使得这种以前致命的肿瘤的总生存率达到70%至90%。CCSK以其模仿和被模仿的能力而闻名于世,它具有独特的转移模式和分子畸变,以及普遍一致的临床表现,这在鉴别中非常有用。一例CCSK在一个4个月大的男孩提出,只有第五例报告的患者年龄小于6个月。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Too Young for Clear Cell Sarcoma of the Kidney? A Case Report With Review of Differential Considerations
Abstract Clear cell sarcoma of the kidney (CCSK) comprises 3% of all childhood renal cancers. Accurate diagnosis is vital for appropriate therapy, which results in a 70% to 90% overall survival rate in this previously lethal tumor. Renowned for its ability to mimic and be mimicked by every other pediatric renal tumor, and even some extrarenal retroperitoneal tumors, CCSK has a unique metastatic pattern and molecular aberrations, as well as a generally consistent clinical presentation which is of great utility in the differential. A case of CCSK in a 4-month-old boy is presented, only the fifth case reported in a patient younger than 6 months.
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CiteScore
0.30
自引率
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