Unilateral absence of the Fallopian tube and ovary with ipsilateral renal agenesis

A 36-year-old primiparous woman with one living child presented to our facility with 4 years history of secondary infertility and 20 weeks gestational age sized painful solid pelvic mass. Ultrasound scan, hysterosalpingography and intravenous urography revealed degenerated fibroids, bilateral tubal occlusion and single ectopic right pelvic kidney. Laparotomy revealed the absence of the left ovary and fallopian tube. This is a very rare finding. Whenever unilateral renal agenesis is found, the patient should be investigated for possible genital anomaly.