M. Gruca, Zakopane Poland Rehabilitation, B. Jasiewicz, T. Potaczek
{"title":"梅干腹综合征的骨科问题- 1例报告","authors":"M. Gruca, Zakopane Poland Rehabilitation, B. Jasiewicz, T. Potaczek","doi":"10.31139/CHNRIOP.2018.83.4.29","DOIUrl":null,"url":null,"abstract":"Prune belly syndrome is a rare congenital syndrome of unknown etiology. It consists of three symptoms: total or partial absence of abdominal muscles, cryptorchismus, and genitourinary malformations. The goal of this study is an analysis of prune belly syndrome patients treated in one hospital. Material: between 2008 and 2017 authors treated 3 patients with prune belly syndrome. A retrospective analysis of medical history of these patients was performed, basing on patients’ data and images available in hospital archive. One patient was treated due to club-foot deformity and lower limb length inequality. Other two were treated for scoliosis, of which one received growth sparing technique, and the other posterior spinal fusion. In all cases the goals of treatment were achieved, no serious complications were noted. Conclusion: patients with prune-belly syndrome may also require orthopedic treatment. Multiple congenital anomalies, eg foot, spine or rib cage deformities may necessitate surgical treatment. Despite of higher risk of pulmonary complications, surgery might be uneventful.","PeriodicalId":89713,"journal":{"name":"Polish orthopedics and traumatology","volume":"1 1","pages":""},"PeriodicalIF":0.0000,"publicationDate":"2018-08-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":"{\"title\":\"Orthopedic problems in prune belly syndrome – case report\",\"authors\":\"M. Gruca, Zakopane Poland Rehabilitation, B. Jasiewicz, T. Potaczek\",\"doi\":\"10.31139/CHNRIOP.2018.83.4.29\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Prune belly syndrome is a rare congenital syndrome of unknown etiology. It consists of three symptoms: total or partial absence of abdominal muscles, cryptorchismus, and genitourinary malformations. The goal of this study is an analysis of prune belly syndrome patients treated in one hospital. Material: between 2008 and 2017 authors treated 3 patients with prune belly syndrome. A retrospective analysis of medical history of these patients was performed, basing on patients’ data and images available in hospital archive. One patient was treated due to club-foot deformity and lower limb length inequality. Other two were treated for scoliosis, of which one received growth sparing technique, and the other posterior spinal fusion. In all cases the goals of treatment were achieved, no serious complications were noted. Conclusion: patients with prune-belly syndrome may also require orthopedic treatment. Multiple congenital anomalies, eg foot, spine or rib cage deformities may necessitate surgical treatment. Despite of higher risk of pulmonary complications, surgery might be uneventful.\",\"PeriodicalId\":89713,\"journal\":{\"name\":\"Polish orthopedics and traumatology\",\"volume\":\"1 1\",\"pages\":\"\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2018-08-30\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"1\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Polish orthopedics and traumatology\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.31139/CHNRIOP.2018.83.4.29\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Polish orthopedics and traumatology","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.31139/CHNRIOP.2018.83.4.29","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Orthopedic problems in prune belly syndrome – case report
Prune belly syndrome is a rare congenital syndrome of unknown etiology. It consists of three symptoms: total or partial absence of abdominal muscles, cryptorchismus, and genitourinary malformations. The goal of this study is an analysis of prune belly syndrome patients treated in one hospital. Material: between 2008 and 2017 authors treated 3 patients with prune belly syndrome. A retrospective analysis of medical history of these patients was performed, basing on patients’ data and images available in hospital archive. One patient was treated due to club-foot deformity and lower limb length inequality. Other two were treated for scoliosis, of which one received growth sparing technique, and the other posterior spinal fusion. In all cases the goals of treatment were achieved, no serious complications were noted. Conclusion: patients with prune-belly syndrome may also require orthopedic treatment. Multiple congenital anomalies, eg foot, spine or rib cage deformities may necessitate surgical treatment. Despite of higher risk of pulmonary complications, surgery might be uneventful.