Bilateral Single System Ectopic Ureters With Ureterocele: A Rare Association in an Adult Male

Bilateral single system ectopic ureter (BSSEU) is a rare congenital malformation. We report a case of BSSEU with a rare association of ectopic ureter with contralateral ectopic sphinctero-stenotic ureterocele with agenesis of one seminal vesicle with normal urinary continence and fertility presenting in adulthood as a case of chronic kidney disease. Diagnosis of ureterocele was missed even after detailed radiological investigations, so concurrent endoscopic evaluation is important for final diagnosis and operative intervention. As renal functions were markedly deranged, so transurethral incision of the right ureterocele with double J stenting was done as a preliminary procedure. Renal functions improved subsequently. Patient is planned for left nephroureterectomy and if necessary right ureteric reimplantation as a secondary major surgery in the follow-up period. World J Nephrol Urol. 2014;3(2):103-105 doi: http://dx.doi.org/10.14740 /wjnu162w