S. Huh, So-Young Lee, Jin-Hyung Lee, Won Gu Lee, Jong Kuk Kim, Yoon Bw, Nam Jun Kim
{"title":"具有抗神经节苷复合物抗体的变异型格林-巴勒综合征","authors":"S. Huh, So-Young Lee, Jin-Hyung Lee, Won Gu Lee, Jong Kuk Kim, Yoon Bw, Nam Jun Kim","doi":"10.18700/JNC.180073","DOIUrl":null,"url":null,"abstract":"Background: Recently, anti-ganglioside complex (GSC) antibodies were discovered among the various subtypes of Guillain-Barré syndrome. GSC is the novel glycoepitopes formed by two individual ganglioside molecules. Case Report: We present a 36-year-old man with overlap Miller Fisher syndrome and acute bulbar palsy who had anti-GSC antibody that provided diagnostic robustness. Conclusion: Anti-GSC testing could be considered important in patients who show atypical manifestation with negative antibody reaction against each constituent ganglioside. J Neurocrit Care 2018;11(2):134-136","PeriodicalId":33246,"journal":{"name":"Journal of Neurocritical Care","volume":" ","pages":""},"PeriodicalIF":0.0000,"publicationDate":"2018-12-27","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"2","resultStr":"{\"title\":\"A Variant Guillain-Barré Syndrome with Anti-Ganglioside Complex Antibody\",\"authors\":\"S. Huh, So-Young Lee, Jin-Hyung Lee, Won Gu Lee, Jong Kuk Kim, Yoon Bw, Nam Jun Kim\",\"doi\":\"10.18700/JNC.180073\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Background: Recently, anti-ganglioside complex (GSC) antibodies were discovered among the various subtypes of Guillain-Barré syndrome. GSC is the novel glycoepitopes formed by two individual ganglioside molecules. Case Report: We present a 36-year-old man with overlap Miller Fisher syndrome and acute bulbar palsy who had anti-GSC antibody that provided diagnostic robustness. Conclusion: Anti-GSC testing could be considered important in patients who show atypical manifestation with negative antibody reaction against each constituent ganglioside. J Neurocrit Care 2018;11(2):134-136\",\"PeriodicalId\":33246,\"journal\":{\"name\":\"Journal of Neurocritical Care\",\"volume\":\" \",\"pages\":\"\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2018-12-27\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"2\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Journal of Neurocritical Care\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.18700/JNC.180073\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q4\",\"JCRName\":\"Nursing\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Journal of Neurocritical Care","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.18700/JNC.180073","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"Nursing","Score":null,"Total":0}
A Variant Guillain-Barré Syndrome with Anti-Ganglioside Complex Antibody
Background: Recently, anti-ganglioside complex (GSC) antibodies were discovered among the various subtypes of Guillain-Barré syndrome. GSC is the novel glycoepitopes formed by two individual ganglioside molecules. Case Report: We present a 36-year-old man with overlap Miller Fisher syndrome and acute bulbar palsy who had anti-GSC antibody that provided diagnostic robustness. Conclusion: Anti-GSC testing could be considered important in patients who show atypical manifestation with negative antibody reaction against each constituent ganglioside. J Neurocrit Care 2018;11(2):134-136