一颗奇怪的心

Marinha Silva, Vitor Hugo Pereira, Alexandra Sousa
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引用次数: 0

摘要

[24]王晓东,王晓东,王晓东,等。Brugada综合征临床症状患者的右心室纤维化和传导延迟:电生理、遗传、组织病理学和计算研究发行量2005;112:2769 - 77。布肯斯街M座25号。Brugada综合征心律失常的发生机制。中国生物医学工程学报(英文版);2020;21(1):591 - 591。Brugada心电图模式是通道病变、结构性心脏病的标志,还是两者都不是?探讨Brugada综合征的统一机制。中国心律失常电生理杂志2010;3:283-90。[27]李建军,李建军,李建军,等。Brugada综合征的磁共振检查显示出乎意料的高结构异常率。[J] .中华医学杂志,2009;30(3):391 - 391。[28]王晓明,王晓明,王晓明,等。Brugada综合征的纤维化、连接蛋白43和传导异常。[J]中华医学杂志,2015;16(6):396 - 396。[29]刘建军,刘建军,李建军,等。临床和遗传学结果对年轻Brugada综合征患者治疗的影响。心脏节律2016;13:1274-82。[30]张建军,张建军,张建军,等。Brugada综合征心律失常多中心调查中的发热相关心律失常心脏节律2018;15:1394-401。[31]钟凤凤,李建平,林玉军,等。一种增强Brugada综合征表型、心外膜功能底物和室性心动过速的新方法。心脏节律2017;14:508-17。[32]李建军,李建军,李建军,等。全胃试验作为一种新的诊断技术,用于识别有Brugada综合征风险的患者。[J]中华心血管病杂志,2006;17(6):591 - 591。[33]王晓明,王晓明,王晓明,等。Brugada综合征患者ST段抬高的自主和抗心律失常药物调节。[J]中华医学杂志1996;27:1061-70。34 . jon C, Gollob MH. Brugada综合征:让我们来谈谈性。心脏节律2018;15:14 . 66 - 7。[35]李建军,李建军,李建军,等。Brugada综合征患者植入心律转复除颤器后的预后:一项多中心研究(2)发行量2013;128:1739-47。[6]王晓明,王晓明,王晓明,等。Brugada综合征猝死病例中危险标志物的低流行率与Brugada综合征的风险分层相关[J]中华医学杂志,2011;37(5):544 - 544。[3]张建军,张建军,张建军,等。程序性心室刺激对Brugada综合征风险分层的影响:一项汇总分析。发行量2016;133:622-30。[38]刘建军,刘建军,刘建军,等。Brugada综合征的风险分层:现状和新兴方法。心律失常电生理学报,2018;7:79。[39]李建平,陈海燕,李建平,等。SCN5A突变类型决定了钠通道病丧失功能的临床严重程度和传导减慢程度。心脏节律2009;6:341-8。2017 AHA/ACC/HRS室性心律失常患者的管理和心脏性猝死的预防指南。发行量2018;138:e272 - 391。[4]李建平,李建平,李建平。使用多基因风险评分预测钠通道阻断和Brugada综合征的心电反应。[J] .中华医学杂志,2019;39(4):391 - 391。[4]张建军,张建军,张建军,等。Brugada综合征患者一级预防临床风险评分模型(BRUGADARISK)中华医学杂志(英文版);2021;7:210-22。[43]李建军,刘建军,刘建军,等。Brugada综合征患者心源性猝死预测评分的稳健性和相关性[J] .中国生物医学工程学报(英文版);2009;32(2):391 - 391。[4]吴琦,波西马,王晓明,等。SARSCoV2、covid - 19和遗传性心律失常综合征。心脏节律2020;17:14 . 56 - 62。[45]李建平,王志强,王志强,等。HRS/EHRA/APHRS关于遗传性原发性心律失常综合征患者诊断和管理的专家共识声明:HRS、EHRA和APHRS于2013年5月批准,ACCF、AHA、PACES和AEPC于2013年6月批准。心脏节律2013;10:193263。[46]王尔德,王尔德,王尔德,等。Brugada综合征晕厥:患病率,临床意义,以及从历史上区分心律失常和非心律失常原因的线索。心律2015;12:367-75。[4]刘建军,刘建军,刘建军。2018 ESC晕厥诊断和治疗指南。欧洲心脏杂志2018;39。[8]李建军,李建军,李建军,等。Brugada综合征儿童和青少年的植入式心律转复除颤器。[J]中国医学杂志,2018;31(1):1 - 4。[4]王晓明,王晓明,王晓明,等。无法获得奎尼丁治疗的情况将变得更糟。中华医学杂志,2013;32(2):355。[5]王晓明,王晓明,王晓明,等。连续135例Brugada综合征患者的电底物消除。心律失常电生理学报,2017;10:1-13。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
A strange heart
24 Coronel R, Casini S, Koopmann TT, et al. Right ventricular fibrosis and conduction delay in a patient with clinical signs of Brugada syndrome: a combined electrophysiological, genetic, histopathologic, and computational study. Circulation 2005;112:2769–77. 25 Blok M, Boukens BJ. Mechanisms of arrhythmias in the Brugada syndrome. Int J Mol Sci 2020;21:7051–20. 26 Hoogendijk MGet al. The Brugada ECG pattern a marker of channelopathy, structural heart disease, or neither? Toward a unifying mechanism of the Brugada syndrome. Circ. Arrhythmia Electrophysiol 2010;3:283–90. 27 Catalano O, Antonaci S, Moro G, et al. Magnetic resonance investigations in Brugada syndrome reveal unexpectedly high rate of structural abnormalities. Eur Heart J 2009;30:2241–8. 28 Nademanee K, Raju H, de Noronha SV, et al. Fibrosis, connexin43, and conduction abnormalities in the Brugada syndrome. J Am Coll Cardiol 2015;66:1976–86. 29 Andorin A, Behr ER, Denjoy I, et al. Impact of clinical and genetic findings on the management of young patients with Brugada syndrome. Heart Rhythm 2016;13:1274–82. 30 Michowitz Y, Milman A, SarquellaBrugada G, et al. Feverrelated arrhythmic events in the multicenter survey on arrhythmic events in Brugada syndrome. Heart Rhythm 2018;15:1394–401. 31 Chung FP, Raharjo SB, Lin YJ, et al. A novel method to enhance phenotype, epicardial functional substrates, and ventricular tachyarrhythmias in Brugada syndrome. Heart Rhythm 2017;14:508–17. 32 Ikeda T, Abe A, Yusu S, et al. The full stomach test as a novel diagnostic technique for identifying patients at risk of Brugada syndrome. J Cardiovasc Electrophysiol 2006;17:602–7. 33 Miyazaki T, Mitamura H, Miyoshi S, et al. Autonomic and antiarrhythmic drug modulation of ST segment elevation in patients with Brugada syndrome. J Am Coll Cardiol 1996;27:1061–70. 34 Jons C, Gollob MH. Brugada syndrome: Let’s talk about sex. Heart Rhythm 2018;15:1466–7. 35 Sacher F, Probst V, Maury P, et al. Outcome after implantation of a cardioverterdefibrillator in patients with Brugada syndrome: a multicenter studypart 2. Circulation 2013;128:1739–47. 36 Raju H, Papadakis M, Govindan M, et al. Low prevalence of risk markers in cases of sudden death due to Brugada syndrome relevance to risk stratification in Brugada syndrome. J Am Coll Cardiol 2011;57:2340–5. 37 Sroubek J, Probst V, Mazzanti A, et al. Programmed ventricular stimulation for risk stratification in the Brugada syndrome: a pooled analysis. Circulation 2016;133:622–30. 38 Honarbakhsh S, Providencia R, Lambiase PD. Risk stratification in Brugada syndrome: current status and emerging approaches. Arrhythm Electrophysiol Rev 2018;7:79. 39 Meregalli PG, Tan HL, Probst V, et al. Type of SCN5A mutation determines clinical severity and degree of conduction slowing in lossoffunction sodium channelopathies. Heart Rhythm 2009;6:341–8. 40 AlKhatib SMet al. 2017 AHA/ACC/HRS guideline for management of patients with ventricular arrhythmias and the prevention of sudden cardiac death. Circulation 2018;138:e272–391. 41 Tadros R, Tan HL, Mathari SE. Predicting cardiac electrical response to sodiumchannel blockade and Brugada syndrome using polygenic risk scores. Eur Heart J 2019;40:3097–107. 42 Honarbakhsh S, Providencia R, GarciaHernandez J, et al. A primary prevention clinical risk score model for patients with Brugada syndrome (BRUGADARISK). JACC Clin Electrophysiol 2021;7:210–22. 43 Probst V, Goronflot T, Anys S, et al. Robustness and relevance of predictive score in sudden cardiac death for patients with Brugada syndrome. Eur Heart J 2021;42:1687–95. 44 Wu CI, Postema PG, Arbelo E, et al. SARSCoV2, COVID19, and inherited arrhythmia syndromes. Heart Rhythm 2020;17:1456–62. 45 Priori SG, Wilde AA, Horie M, et al. HRS/EHRA/APHRS expert consensus statement on the diagnosis and management of patients with inherited primary arrhythmia syndromes: document endorsed by Hrs, EHRA, and APHRS in May 2013 and by ACCF, AHA, PACES, and AEPC in June 2013. Heart Rhythm 2013;10:193263. 46 Olde Nordkamp LRA, Vink AS, Wilde AAM, et al. Syncope in Brugada syndrome: prevalence, clinical significance, and clues from history taking to distinguish arrhythmic from nonarrhythmic causes. Heart Rhythm 2015;12:367–75. 47 Brignole M, Moya A, Lange FJde. 2018 ESC guidelines for the diagnosis and management of syncope. Eur Heart J 2018;39. 48 Gonzalez Corcia MC, Sieira J, Pappaert G, et al. Implantable CardioverterDefibrillators in Children and Adolescents With Brugada Syndrome. J Am Coll Cardiol 2018;71:148–57. 49 Viskin S, Wilde AAM, Krahn AD, et al. Inaccessibility to quinidine therapy is about to get worse. J Am Coll Cardiol 2013;62:355. 50 Pappone C, Brugada J, Vicedomini G, et al. Electrical substrate elimination in 135 consecutive patients with Brugada syndrome. Circ Arrhythm Electrophysiol 2017;10:1–13.
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