K. Maduranga, D. Jayarathne, K. Thebuwana, L. Wijekoon, V. Mendis, H. Senanayake, S. Siribaddana
{"title":"早期血浆交换治疗超急性肝功能衰竭所致噬血细胞淋巴组织细胞增多症的成功一份病例报告和已发表病例的回顾。","authors":"K. Maduranga, D. Jayarathne, K. Thebuwana, L. Wijekoon, V. Mendis, H. Senanayake, S. Siribaddana","doi":"10.4038/amj.v17i2.7754","DOIUrl":null,"url":null,"abstract":"Hemophagocytic lymphohistiocytosis (HLH) is a rare severe inflammatory syndrome of excessive cytokine production. A 16-year-old girl presented with hyperacute liver failure due to idiopathic HLH. Liver failure due to HLH is uncommon, and survival in an adult after hyperacute liver failure is rare. Early diagnosis of the disease and timely treatment with plasma exchange followed by immunosuppressive therapy were associated with the survival of this patient.","PeriodicalId":30600,"journal":{"name":"Anuradhapura Medical Journal","volume":" ","pages":""},"PeriodicalIF":0.0000,"publicationDate":"2023-07-21","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Successful early plasma exchange therapy in hemophagocytic lymphohistiocytosis due to hyperacute liver failure; A case report and review of published cases.\",\"authors\":\"K. Maduranga, D. Jayarathne, K. Thebuwana, L. Wijekoon, V. Mendis, H. Senanayake, S. Siribaddana\",\"doi\":\"10.4038/amj.v17i2.7754\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Hemophagocytic lymphohistiocytosis (HLH) is a rare severe inflammatory syndrome of excessive cytokine production. A 16-year-old girl presented with hyperacute liver failure due to idiopathic HLH. Liver failure due to HLH is uncommon, and survival in an adult after hyperacute liver failure is rare. Early diagnosis of the disease and timely treatment with plasma exchange followed by immunosuppressive therapy were associated with the survival of this patient.\",\"PeriodicalId\":30600,\"journal\":{\"name\":\"Anuradhapura Medical Journal\",\"volume\":\" \",\"pages\":\"\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2023-07-21\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Anuradhapura Medical Journal\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.4038/amj.v17i2.7754\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Anuradhapura Medical Journal","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4038/amj.v17i2.7754","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Successful early plasma exchange therapy in hemophagocytic lymphohistiocytosis due to hyperacute liver failure; A case report and review of published cases.
Hemophagocytic lymphohistiocytosis (HLH) is a rare severe inflammatory syndrome of excessive cytokine production. A 16-year-old girl presented with hyperacute liver failure due to idiopathic HLH. Liver failure due to HLH is uncommon, and survival in an adult after hyperacute liver failure is rare. Early diagnosis of the disease and timely treatment with plasma exchange followed by immunosuppressive therapy were associated with the survival of this patient.
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