嗜酸性肉芽肿病合并多血管炎(churg-strauss, EGPA) 1例，表现为复发性多发性单神经炎

IF 0.3 Q3 MEDICINE, GENERAL & INTERNAL

International Medical Journal Malaysia Pub Date : 2020-11-09 DOI:10.31436/IMJM.V13I1.496

Hilmi Abdullah, M. Ainon

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引用次数: 0

摘要

我们报告一例嗜酸性肉芽肿病合并多血管炎(EGPA)，这是一种罕见的多系统疾病，以难以控制的哮喘、嗜酸性粒细胞增多和多神经病变为特征。我们还讨论了五因子评分(FFS)风险分层策略，该策略用于量化疾病的程度并指导治疗策略。关键词:丘格-施特劳斯综合征，血管炎，多发性单神经炎，环磷酰胺

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A case of eosinophilic granulomatosis with polyangiitis (churg-strauss, EGPA) presenting with relapsed mononeuritis multiplex

ABSTRACT We report a case of eosinophilic granulomatosis with polyangiitis (EGPA), a rare multisystem disorder characterized by difficult-to-control asthma, hypereosinophilia and polyneuropathy. We also discuss the Five Factor Score (FFS) risk stratification strategy, which is used to quantitate the extent of the disease and guide treatment strategy. KEYWORDS: Churg-Strauss syndrome, vasculitis, mononeuritis multiplex, cyclophosphamide

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来源期刊

International Medical Journal Malaysia Medicine-Medicine (all)

CiteScore

0.40

自引率

0.00%

发文量

期刊介绍： International Medical Journal Malaysia (IMJM) is the official journal of the Kulliyyah (Faculty) of Medicine, International Islamic University Malaysia. It serves primarily as a forum for education and intellectual discourse for health professionals namely in clinical medicine but covers diverse issues relating to medical ethics, professionalism as well as medical developments and research in basic medical sciences. It also serves the unique purpose of highlighting issues and research pertaining to the Muslim world. Contributions to the IMJM reflect its international and multidisciplinary readership and include current thinking across a range of specialties, ethnicities and societies.