系统性青少年特发性关节炎发病机制的分子途径。

IF 2.6 4区 医学 Q2 RHEUMATOLOGY
Grant S. Schulert MD, PhD , Christoph Kessel PhD
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引用次数: 2

摘要

系统性青少年特发性关节炎(sJIA)是一种罕见的儿童慢性炎症性疾病,有可能引发危及生命的并发症,包括巨噬细胞活化综合征和肺病。发病时,sJIA的发病机制类似于自身炎症性周期性发热综合征,具有明显的先天免疫激活、中性粒细胞和单核细胞的扩张以及高水平的白细胞介素-18。在此,我们回顾了目前对sJIA发病机制的概念性理解,重点关注先天免疫途径和适应性免疫途径。最后,我们考虑最近在理解sJIA的免疫学基础方面的进展如何支持难治性疾病的新疗法。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Molecular Pathways in the Pathogenesis of Systemic Juvenile Idiopathic Arthritis
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来源期刊
CiteScore
4.20
自引率
0.00%
发文量
84
审稿时长
>12 weeks
期刊介绍: Rheumatic Disease Clinics updates you on the latest trends in patient management, keeps you up to date on the newest advances, and provides a sound basis for choosing treatment options. Each issue (February, May, August, and November) focuses on a single topic in rheumatology and is presented under the direction of an experienced editor. Topics include osteoarthritis, rheumatoid arthritis, crystal diseases, MSK exam, disorders of the bone, immunodeficiency states, lupus, neuromuscular disease, pain disorders, scleroderma, vasculitis, pediatrics, therapeutics, treatment guidelines, and treatment modalities.
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