Caroline Melou, Nicolas Taillard, Dominique Chauvel-Lebret
{"title":"[埃勒斯-丹洛斯综合症:牙医的角色]。","authors":"Caroline Melou, Nicolas Taillard, Dominique Chauvel-Lebret","doi":"10.1684/orthodfr.2021.51","DOIUrl":null,"url":null,"abstract":"<p><p>The Ehlers-Danlos syndrome (EDS) is a group of genetic connective tissue disorder due to abnormal collagen synthesis. EDS is characterized by the triad: joint hypermobility - skin hyperextensibility - connective tissue friability leading to vascular and skin fragility. Thirteen forms exist including three main ones: the hypermobile, classical and vascular forms. Given the diversity of clinical manifestations, the diagnosis of EDS is difficult. The management of this syndrome is multidisciplinary and includes the dental surgeon, because EDS can have many oral and dental manifestations. This syndrome can lead to dental, periodontal, mucosal damage and also to joint damage to the manducatory apparatus. The authors, after describing the symptoms of EDS, their manifestations and their detection, will explain the implications in odontostomatology. EDS must be known to the dentist because it can lead to precautions during dental care, and because patients with EDS are more prone to temporomandibular disorders. At the last, the many oral and dental manifestations of EDS give the dentist an important role in screening for this syndrome.</p>","PeriodicalId":35927,"journal":{"name":"L'' Orthodontie française","volume":"92 3","pages":"367-375"},"PeriodicalIF":0.0000,"publicationDate":"2021-09-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":"{\"title\":\"[Ehlers-Danlos syndrome: Role of the dentist].\",\"authors\":\"Caroline Melou, Nicolas Taillard, Dominique Chauvel-Lebret\",\"doi\":\"10.1684/orthodfr.2021.51\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>The Ehlers-Danlos syndrome (EDS) is a group of genetic connective tissue disorder due to abnormal collagen synthesis. EDS is characterized by the triad: joint hypermobility - skin hyperextensibility - connective tissue friability leading to vascular and skin fragility. Thirteen forms exist including three main ones: the hypermobile, classical and vascular forms. Given the diversity of clinical manifestations, the diagnosis of EDS is difficult. The management of this syndrome is multidisciplinary and includes the dental surgeon, because EDS can have many oral and dental manifestations. This syndrome can lead to dental, periodontal, mucosal damage and also to joint damage to the manducatory apparatus. The authors, after describing the symptoms of EDS, their manifestations and their detection, will explain the implications in odontostomatology. EDS must be known to the dentist because it can lead to precautions during dental care, and because patients with EDS are more prone to temporomandibular disorders. At the last, the many oral and dental manifestations of EDS give the dentist an important role in screening for this syndrome.</p>\",\"PeriodicalId\":35927,\"journal\":{\"name\":\"L'' Orthodontie française\",\"volume\":\"92 3\",\"pages\":\"367-375\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2021-09-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"1\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"L'' Orthodontie française\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.1684/orthodfr.2021.51\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q4\",\"JCRName\":\"Medicine\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"L'' Orthodontie française","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.1684/orthodfr.2021.51","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"Medicine","Score":null,"Total":0}
The Ehlers-Danlos syndrome (EDS) is a group of genetic connective tissue disorder due to abnormal collagen synthesis. EDS is characterized by the triad: joint hypermobility - skin hyperextensibility - connective tissue friability leading to vascular and skin fragility. Thirteen forms exist including three main ones: the hypermobile, classical and vascular forms. Given the diversity of clinical manifestations, the diagnosis of EDS is difficult. The management of this syndrome is multidisciplinary and includes the dental surgeon, because EDS can have many oral and dental manifestations. This syndrome can lead to dental, periodontal, mucosal damage and also to joint damage to the manducatory apparatus. The authors, after describing the symptoms of EDS, their manifestations and their detection, will explain the implications in odontostomatology. EDS must be known to the dentist because it can lead to precautions during dental care, and because patients with EDS are more prone to temporomandibular disorders. At the last, the many oral and dental manifestations of EDS give the dentist an important role in screening for this syndrome.
期刊介绍:
L’Orthodontie Française, organe officiel de communication de la Société Française d’Orthopédie Dento-Faciale, est un journal scientifique de référence depuis 1921, de diffusion internationale, indexé à Medline et référencé à l’Index Medicus et à Bibliodent. Le journal a pour vocation d’accueillir les travaux des membres de la SFODF, des conférenciers ayant communiqué lors des congrès de la Société, ou de tout travail soumis à l’approbation de son comité de rédaction, traitant de l’orthopédie dento-faciale ou de tout sujet en rapport avec cette discipline.