R. Caiazzo , C. Mariette , G. Piessen , T. Jany , B. Carnaille , J.-P. Triboulet
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引用次数: 9
摘要
Von Recklinghausen神经纤维瘤病(常染色体显性遗传病)累及胃肠道见于25%的患者,常表现为十二指肠类癌。我们报告一例42岁女性壶腹生长抑素瘤合并神经纤维瘤病和嗜铬细胞瘤,并对神经纤维瘤病和生长抑素瘤的相关文献进行综述。这种病理联系似乎没有危险,手术壶胃切除术在局部肿瘤治疗中提供了胰十二指肠切除术的良好选择。
Association neurofibromatose de type I, phéochromocytome et somatostatinome de l'ampoule de Vater. Revue de la littérature
Gastrointestinal involvement in Von Recklinghausen's neurofibromatosis (autosomal dominant disease) is observed in 25% of patients and is frequently represented by duodenal carcinoids. We report a case of somatostatinoma of the ampulla in a 42-year-old female with neurofibromatosis and pheochromocytoma and show a literature review about the association of neurofibromatosis and somatostatinoma. This pathological association appears non hasardous and surgical ampullectomy offers a good alternative to pancreaticoduodenectomy in localised tumors treatment.