3小血管血管炎和局限于皮肤的血管炎

MD Cem Mat (Professor of Dermatology), MD Sebahattin Yurdakul (Professor of Medicine), MD Nükhet Tüzüner (Professor of Pathology), MD Yalçin Tüzün (Professor of Dermatology)
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引用次数: 11

摘要

皮肤血管炎是一组异质性疾病,可局限于皮肤或可能是相关的全身性疾病的一部分。各种病因以及类似皮肤血管炎的情况,通常表现出相似的临床特征;主要是可触性紫癜。皮肤活检通常显示白细胞破裂性血管炎。这对医生的诊断和治疗提出了巨大的挑战。本文综述了各种形式(药物、感染、恶性肿瘤、全身性血管炎、结缔组织疾病、Schönlein-Henoch紫癜、冷球蛋白血症、结节性皮肤动脉周炎、类血管炎、高脂血肿和荨麻疹血管炎)的病因、临床特征、诊断和治疗方法。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
3 Small vessel vasculitis and vasculitis confined to skin

Cutaneous vasculitis is a heterogeneous group of disorders, which can be confined to the skin or may be part of an associated systemic disease. Various aetiological agents as well as conditions that mimic skin vasculitis, usually present with similar clinical features; mainly palpable purpura. The skin biopsies usually show leukocytoclastic vasculitis. This poses a great diagnostic and therapeutic challenge for the physician. The aetiologies, clinical features, diagnosis and treatment modalities for each form (drugs, infections, malignancies, systemic vasculitides, connective tissue disorders, Schönlein-Henoch purpura, cryoglobulinaemia, cutaneous periarteritis nodosa, livedoid vasculitis, erythema elevatum diutinum and urticarial vasculitis) are reviewed.

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