布劳氏综合征与结节病的比较。

Sarcoidosis Pub Date : 1994-09-01
D G James
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引用次数: 0

摘要

Blau综合征是一种家族性多系统肉芽肿性炎症,可与儿童结节病混淆,因为它表现为虹膜睫状体炎、后葡萄膜炎、肉芽肿性皮肤病、关节炎和血清血管紧张素转换酶升高。他们的特点是没有肺部受累和Kveim-Siltzbach皮肤试验阴性。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
A comparison of Blau's syndrome and sarcoidosis.

Blau's syndrome is a familial multisystem granulomatous inflammation which may be confused with childhood sarcoidosis because it presents with iridocyclitis, posterior uveitis, granulomatous skin disease, arthritis and elevated serum angiotensin-converting enzyme. They are distinguished by the absence of pulmonary involvement and a negative Kveim-Siltzbach skin test.

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