右心房附件在法洛四联症患儿肺瓣膜缺失中的应用。

IF 0.8 Q4 CARDIAC & CARDIOVASCULAR SYSTEMS

Annals of Pediatric Cardiology Pub Date : 2026-05-01 Epub Date: 2026-06-23 DOI:10.4103/apc.apc_220_25

Amitabh Satsangi, Srinivas Thimmasarthi, Arindam Choudhury, B Kanmaniyan, Pratik K Jha

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引用次数: 0

摘要

肺动脉瓣缺失是一种罕见的先天性心脏异常，常与法洛四联症有关。我们提出的情况下，一个12岁的孩子谁来的紫绀和心脏杂音的症状。超声心动图评估显示严重的漏斗状肺狭窄和主动脉下室间隔缺损。术中发现证实存在一个初步的肺瓣膜，其薄的索样结构与残余的肺小叶相连。该患儿接受了成功的心内修复，其中包括利用右心房附件组织重建新的肺瓣膜。

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Right atrial appendage for neopulmonary valve reconstruction in a child with tetralogy of Fallot with absent pulmonary valve.

Absent pulmonary valve is a rare congenital heart anomaly frequently associated with tetralogy of Fallot. We present the case of a 12-year-old child who came with symptoms of cyanosis and a heart murmur. Echocardiographic evaluation revealed severe infundibular pulmonary stenosis and a large subaortic ventricular septal defect. Intraoperative findings confirmed the presence of a rudimentary pulmonary valve, with thin, chordae-like structures connected to the pulmonary leaflet remnants. The child underwent successful intracardiac repair, which involved the reconstruction of a neopulmonary valve utilizing the right atrial appendage tissue.

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