{"title":"一种罕见的混合全异常肺静脉连接与奇系花环结构的变异:扩大了解剖变异的频谱。","authors":"Chigurupati Bharat Siddharth, Pavan Kumar Dammalapati, Venkata Rama Muddana Subramanyam, Hareesh Kumar Munugala, Vasudev Vemala","doi":"10.4103/apc.apc_285_25","DOIUrl":null,"url":null,"abstract":"<p><p>Mixed-type total anomalous pulmonary venous connection (TAPVC) is the least common variant in Darling's classification and is further subdivided into three distinct subtypes. We report an exceptionally rare mixed TAPVC with a 2 + 2 drainage pattern, associated with an unusual venous anomaly in which the hemiazygos vein drains into the innominate vein, forming a characteristic \"garland\" configuration.</p>","PeriodicalId":8026,"journal":{"name":"Annals of Pediatric Cardiology","volume":"18 6","pages":"635-637"},"PeriodicalIF":0.7000,"publicationDate":"2025-11-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13048706/pdf/","citationCount":"0","resultStr":"{\"title\":\"A rare variant of mixed total anomalous pulmonary venous connection with a garland configuration of the azygous system: Expanding the spectrum of anatomical variants.\",\"authors\":\"Chigurupati Bharat Siddharth, Pavan Kumar Dammalapati, Venkata Rama Muddana Subramanyam, Hareesh Kumar Munugala, Vasudev Vemala\",\"doi\":\"10.4103/apc.apc_285_25\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Mixed-type total anomalous pulmonary venous connection (TAPVC) is the least common variant in Darling's classification and is further subdivided into three distinct subtypes. We report an exceptionally rare mixed TAPVC with a 2 + 2 drainage pattern, associated with an unusual venous anomaly in which the hemiazygos vein drains into the innominate vein, forming a characteristic \\\"garland\\\" configuration.</p>\",\"PeriodicalId\":8026,\"journal\":{\"name\":\"Annals of Pediatric Cardiology\",\"volume\":\"18 6\",\"pages\":\"635-637\"},\"PeriodicalIF\":0.7000,\"publicationDate\":\"2025-11-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13048706/pdf/\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Annals of Pediatric Cardiology\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.4103/apc.apc_285_25\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"2026/3/16 0:00:00\",\"PubModel\":\"Epub\",\"JCR\":\"Q4\",\"JCRName\":\"CARDIAC & CARDIOVASCULAR SYSTEMS\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Annals of Pediatric Cardiology","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4103/apc.apc_285_25","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2026/3/16 0:00:00","PubModel":"Epub","JCR":"Q4","JCRName":"CARDIAC & CARDIOVASCULAR SYSTEMS","Score":null,"Total":0}
A rare variant of mixed total anomalous pulmonary venous connection with a garland configuration of the azygous system: Expanding the spectrum of anatomical variants.
Mixed-type total anomalous pulmonary venous connection (TAPVC) is the least common variant in Darling's classification and is further subdivided into three distinct subtypes. We report an exceptionally rare mixed TAPVC with a 2 + 2 drainage pattern, associated with an unusual venous anomaly in which the hemiazygos vein drains into the innominate vein, forming a characteristic "garland" configuration.