一种罕见的混合全异常肺静脉连接与奇系花环结构的变异:扩大了解剖变异的频谱。

IF 0.7 Q4 CARDIAC & CARDIOVASCULAR SYSTEMS
Annals of Pediatric Cardiology Pub Date : 2025-11-01 Epub Date: 2026-03-16 DOI:10.4103/apc.apc_285_25
Chigurupati Bharat Siddharth, Pavan Kumar Dammalapati, Venkata Rama Muddana Subramanyam, Hareesh Kumar Munugala, Vasudev Vemala
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引用次数: 0

摘要

混合型完全异常肺静脉连接(TAPVC)是Darling分类中最不常见的变体,并进一步细分为三个不同的亚型。我们报告一例罕见的2 + 2引流模式的混合型TAPVC,伴有不寻常的静脉异常,其中半奇静脉流入无名静脉,形成特征性的“花环”结构。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
A rare variant of mixed total anomalous pulmonary venous connection with a garland configuration of the azygous system: Expanding the spectrum of anatomical variants.

Mixed-type total anomalous pulmonary venous connection (TAPVC) is the least common variant in Darling's classification and is further subdivided into three distinct subtypes. We report an exceptionally rare mixed TAPVC with a 2 + 2 drainage pattern, associated with an unusual venous anomaly in which the hemiazygos vein drains into the innominate vein, forming a characteristic "garland" configuration.

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来源期刊
Annals of Pediatric Cardiology
Annals of Pediatric Cardiology CARDIAC & CARDIOVASCULAR SYSTEMS-
CiteScore
1.40
自引率
14.30%
发文量
51
审稿时长
23 weeks
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