Collin M Ainslie, Krishna Patel, Yen T B Tran, Samuel C Bartley, Navaneetha Krishnan Bharathan, Volker Spindler, Alexa L Mattheyses
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引用次数: 0
摘要
桥粒蛋白(Desmoplakin, DP)是桥粒中的一种关键蛋白,桥粒是细胞-细胞连接点,为皮肤和心脏提供机械完整性。DP有三种异构体,DPI, DPIa和DPII,它们的不同之处在于它们的中心棒状结构域的长度,并且是由选择性剪接引起的。组织特异性DP亚型表达的改变是罕见皮肤和心脏疾病的基础。桥粒是大分子复合物,其蛋白质结构对生理功能至关重要。在这里,我们使用dSTORM定义DPI、DPIa和DPII的结构排列,并在DP KO HaCaT细胞中表达c端mEGFP。我们表明,DP尾域位置是同工形相关的,并与杆长相关。DPI的杆状结构域最长,尾距质膜最远,而DPII的杆状结构域最短,尾距质膜最近。这种可变尾位结构在同时表达DPI和DPII的WT HaCaT细胞中是保守的。我们提出了一种新的定向角模型,每个DP异构体相对于质膜以锐角共定向。这些结果为DP架构如何支持桥粒功能提供了见解。
The desmoplakin tail domain position in the desmosomal plaque is isoform dependent.
Desmoplakin (DP, also known as DSP) is a key protein in desmosomes, cell-cell junctions that provide mechanical integrity to the skin and heart. DP has three isoforms, DPI, DPIa and DPII, which differ only in the length of their central rod domain and arise from alternative splicing. Alterations of tissue-specific DP isoform expression underlie rare skin and heart diseases. Desmosomes are macromolecular complexes, and their protein architecture is essential for physiological function. Here, we used direct stochastic optical reconstruction microscopy (dSTORM) to define the architectural arrangement of DPI, DPIa and DPII with a C-terminal mEGFP expressed in DP-knockout (KO) HaCaT cells. We show the DP tail domain position is isoform dependent and correlates with rod length. DPI has the longest rod domain, and its tail is farthest from the plasma membrane, whereas DPII has the shortest rod and is closest. This variable tail location architecture was conserved in wild-type HaCaT cells expressing both DPI and DPII. We propose a novel aligned angle model, with each DP isoform co-aligned at an acute angle relative to the plasma membrane. These results provide insight into how DP architecture supports desmosome function.