专家共识:间质性肺疾病与系统性自身免疫性疾病相关。执行概要。

A González-García, M Akasbi, M P Brito-Zerón, J L Callejas, I Cusacovich, F Jiménez Segovia, M Martín Cascón, S Prieto-González, L Sáez Comet, C P Simeón, R Solans Laque, J S García Morillo
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引用次数: 0

摘要

间质性肺疾病(ILD)是系统性自身免疫性疾病(SAD)的一种常见且可能致命的表现。早期筛查、诊断和免疫调节剂治疗,在某些情况下使用抗纤维化药物,以及适当的随访,对于改善患者的生活质量和生存率至关重要。这些疾病的复杂性和指导临床决策的有限有力证据导致管理指南的显著差异。在这篇文章中,一组SAD的专家考虑到最新的证据、他们的临床经验和一项专家调查的结果,对ILD的筛查、诊断、治疗和随访提出了建议。这些疾病包括系统性硬化症、Sjögren病、特发性炎性肌病、anca相关血管炎、结节病和系统性红斑狼疮。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Expert consensus on interstitial lung disease associated with systemic autoimmune diseases. Executive summary.

Interstitial lung disease (ILD) is a frequent and potentially fatal manifestation of systemic autoimmune diseases (SAD). Early screening, diagnosis, and treatment with immunomodulators, and in some cases, antifibrotics, as well as appropriate follow-up, are essential to improving patients' quality of life and survival. The complexity of these diseases and the limited robust evidence to guide clinical decision-making lead to significant variability in management guidelines. In this article, a group of experts in SAD has developed recommendations for the screening, diagnosis, treatment, and follow-up of ILD, considering the latest evidence, their clinical experience, and the results of a survey conducted among specialists. The diseases included are systemic sclerosis, Sjögren's disease, idiopathic inflammatory myopathy, ANCA-associated vasculitis, sarcoidosis and systemic lupus erythematosus.

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