Jinya Lin, Xiupu Liu, Shuangwei Ying, Yuanyuan Zhu, Weijia Huang, Weiyan Zheng, Xiujin Ye, Jimin Shi, Yi Luo, Jingsong He, Zhen Cai, Yi Zhao, Wenjun Wu, Donghua He, Xiaoyan Han, Gaofeng Zheng, Yanmin Zhao, Yongxian Hu, He Huang, Jie Sun
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引用次数: 0
摘要
根据2022年国际共识分类(ICC)指南,在强化治疗(INT)的急性髓性白血病(AML)中,9个骨髓增生异常相关(mds相关)基因突变被归类为不良风险标志物。尽管venetoclax (VEN)已证明对伴有mds相关基因突变(AML- mr)的AML亚群有临床益处,但其对所有9种突变的疗效仍不清楚。在这项涉及453例AML-MR患者的回顾性研究中,总体复合完全缓解(CRc)率为62.6%(275/439)。在接受INT治疗的适合患者中,57.7%(86/149)在单周期诱导治疗(IND1)后实现结直肠癌,而接受低强度治疗(LIT)的不适合患者中,62.7%(79/126)在IND1后实现结直肠癌。VEN显著改善了接受LIT治疗的不适合患者的CRc发生率(45.9% vs. 30.0%, P = 0.002),但在接受INT治疗的适合患者中没有(61.1% vs. 45.0%, P = 0.052)。在两组中,IND1后的结直肠癌与改善的总生存期(OS)密切相关。亚组分析显示,造血干细胞移植(HSCT)可显著延长无不良风险细胞遗传学患者的OS和无复发生存期(RFS) (OS P = 0.002, P = 0.001)
Selective efficacy of venetoclax in unfit patients with acute myeloid leukemia with myelodysplasia-related gene mutations under low-intensity therapy.
According to the 2022 International Consensus Classification (ICC) guidelines, nine myelodysplasia-related (MDS-related) gene mutations are classified as adverse-risk markers in acute myeloid leukemia (AML) under intensive therapy (INT). Although venetoclax (VEN) has demonstrated clinical benefit in subsets of AML with MDS-related gene mutations (AML-MR), its efficacy across all nine mutations remains unclear. In this retrospective study involving 453 AML-MR patients, the overall composite complete remission (CRc) rate was 62.6% (275/439). Among fit patients receiving INT, 57.7% (86/149) achieved CRc after a single cycle of induction therapy (IND1), while 62.7% (79/126) of unfit patients receiving low-intensity therapy (LIT) achieved CRc after IND1. VEN significantly improved CRc rates in unfit patients treated with LIT (45.9% vs. 30.0%, P = 0.002), but not in fit patients receiving INT (61.1% vs. 45.0%, P = 0.052). In both groups, CRc after IND1 was strongly associated with improved overall survival (OS). Subgroup analysis showed that hematopoietic stem cell transplantation (HSCT) significantly prolonged OS and relapse-free survival (RFS) in patients without favorable-risk cytogenetics (P = 0.002 for OS, P < 0.001 for RFS), but conferred no survival benefit in those with favorable-risk cytogenetics (P = 0.119 for OS, P = 0.437 for RFS). These findings support the use of VEN to enhance early remission and survival outcomes in unfit AML-MR patients and suggest that HSCT should be considered primarily in those lacking favorable-risk cytogenetics.
期刊介绍:
Annals of Hematology covers the whole spectrum of clinical and experimental hematology, hemostaseology, blood transfusion, and related aspects of medical oncology, including diagnosis and treatment of leukemias, lymphatic neoplasias and solid tumors, and transplantation of hematopoietic stem cells. Coverage includes general aspects of oncology, molecular biology and immunology as pertinent to problems of human blood disease. The journal is associated with the German Society for Hematology and Medical Oncology, and the Austrian Society for Hematology and Oncology.