累及脊柱和肋骨的老年多骨性纤维发育不良1例。

IF 0.7 Q4 CARDIAC & CARDIOVASCULAR SYSTEMS
Pinar Çağan, Seyedehtina Safaei, Ali Kimiaei, Cemal Asim Kutlu
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引用次数: 0

摘要

纤维性发育不良(FD)是一种良性骨骼疾病,其特征是正常骨被纤维骨组织取代,常导致骨膨胀和畸形。多骨纤维发育不良(PFD),累及多块骨骼,并不常见,很少影响脊柱和肋骨,文献中报道的病例少于40例。我们提出的情况下,65岁的男性谁提出突然左侧背部疼痛和左侧上睑下垂。影像学显示广泛的FD影响颈胸椎和邻近肋骨。手术切除包括开胸和切除病理性肋骨和脊柱病变。该手术确保了重要结构的保存,并实现了肿瘤的完全切除。手术切除仍然是治疗脊柱和肋骨症状性PFD的关键,目的是完全切除肿瘤。长期随访是监测复发和评估患者预后的必要条件。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Polyostotic fibrous dysplasia in an elderly patient involving spine and ribs.

Fibrous dysplasia (FD) is a benign skeletal disorder characterized by the replacement of normal bone with fibro-osseous tissue, which often causes bone expansion and deformities. Polyostotic fibrous dysplasia (PFD), involving multiple bones, is uncommon and rarely affects the spine and ribs, with fewer than 40 reported cases in the literature. We present the case of a 65-year-old male who presented with sudden left-sided back pain and left sided ptosis. Imaging revealed extensive FD affecting the cervicothoracic vertebrae and the adjacent ribs. Surgical resection involving thoracotomy and excision of the pathological ribs and spinal lesions was performed. The procedure ensured the preservation of vital structures and achieved complete tumor removal. Surgical resection remains crucial in managing symptomatic PFD of the spine and ribs with the aim of complete tumor removal. Long-term follow-up is essential to monitor recurrence and evaluate patient outcomes.

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来源期刊
Indian Journal of Thoracic and Cardiovascular Surgery
Indian Journal of Thoracic and Cardiovascular Surgery CARDIAC & CARDIOVASCULAR SYSTEMS-
CiteScore
1.20
自引率
14.30%
发文量
141
期刊介绍: The primary aim of the Indian Journal of Thoracic and Cardiovascular Surgery is education. The journal aims to dissipate current clinical practices and developments in the area of cardiovascular and thoracic surgery. This includes information on cardiovascular epidemiology, aetiopathogenesis, clinical manifestation etc. The journal accepts manuscripts from cardiovascular anaesthesia, cardiothoracic and vascular nursing and technology development and new/innovative products.The journal is the official publication of the Indian Association of Cardiovascular and Thoracic Surgeons which has a membership of over 1000 at present.DescriptionThe journal is the official organ of the Indian Association of Cardiovascular-Thoracic Surgeons. It was started in 1982 by Dr. Solomon Victor and ws being published twice a year up to 1996. From 2000 the editorial office moved to Delhi. From 2001 the journal was extended to quarterly and subsequently four issues annually have been printed out at time and regularly without fail. The journal receives manuscripts from members and non-members and cardiovascular surgeons. The manuscripts are peer reviewed by at least two or sometimes three or four reviewers who are on the panel. The manuscript process is now completely online. Funding the journal comes partially from the organization and from revenue generated by subscription and advertisement.
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