Pinar Çağan, Seyedehtina Safaei, Ali Kimiaei, Cemal Asim Kutlu
{"title":"累及脊柱和肋骨的老年多骨性纤维发育不良1例。","authors":"Pinar Çağan, Seyedehtina Safaei, Ali Kimiaei, Cemal Asim Kutlu","doi":"10.1007/s12055-024-01842-2","DOIUrl":null,"url":null,"abstract":"<p><p>Fibrous dysplasia (FD) is a benign skeletal disorder characterized by the replacement of normal bone with fibro-osseous tissue, which often causes bone expansion and deformities. Polyostotic fibrous dysplasia (PFD), involving multiple bones, is uncommon and rarely affects the spine and ribs, with fewer than 40 reported cases in the literature. We present the case of a 65-year-old male who presented with sudden left-sided back pain and left sided ptosis. Imaging revealed extensive FD affecting the cervicothoracic vertebrae and the adjacent ribs. Surgical resection involving thoracotomy and excision of the pathological ribs and spinal lesions was performed. The procedure ensured the preservation of vital structures and achieved complete tumor removal. Surgical resection remains crucial in managing symptomatic PFD of the spine and ribs with the aim of complete tumor removal. Long-term follow-up is essential to monitor recurrence and evaluate patient outcomes.</p>","PeriodicalId":13285,"journal":{"name":"Indian Journal of Thoracic and Cardiovascular Surgery","volume":"41 5","pages":"569-573"},"PeriodicalIF":0.7000,"publicationDate":"2025-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC12000474/pdf/","citationCount":"0","resultStr":"{\"title\":\"Polyostotic fibrous dysplasia in an elderly patient involving spine and ribs.\",\"authors\":\"Pinar Çağan, Seyedehtina Safaei, Ali Kimiaei, Cemal Asim Kutlu\",\"doi\":\"10.1007/s12055-024-01842-2\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Fibrous dysplasia (FD) is a benign skeletal disorder characterized by the replacement of normal bone with fibro-osseous tissue, which often causes bone expansion and deformities. Polyostotic fibrous dysplasia (PFD), involving multiple bones, is uncommon and rarely affects the spine and ribs, with fewer than 40 reported cases in the literature. We present the case of a 65-year-old male who presented with sudden left-sided back pain and left sided ptosis. Imaging revealed extensive FD affecting the cervicothoracic vertebrae and the adjacent ribs. Surgical resection involving thoracotomy and excision of the pathological ribs and spinal lesions was performed. The procedure ensured the preservation of vital structures and achieved complete tumor removal. Surgical resection remains crucial in managing symptomatic PFD of the spine and ribs with the aim of complete tumor removal. Long-term follow-up is essential to monitor recurrence and evaluate patient outcomes.</p>\",\"PeriodicalId\":13285,\"journal\":{\"name\":\"Indian Journal of Thoracic and Cardiovascular Surgery\",\"volume\":\"41 5\",\"pages\":\"569-573\"},\"PeriodicalIF\":0.7000,\"publicationDate\":\"2025-05-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC12000474/pdf/\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Indian Journal of Thoracic and Cardiovascular Surgery\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.1007/s12055-024-01842-2\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"2024/10/25 0:00:00\",\"PubModel\":\"Epub\",\"JCR\":\"Q4\",\"JCRName\":\"CARDIAC & CARDIOVASCULAR SYSTEMS\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Indian Journal of Thoracic and Cardiovascular Surgery","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.1007/s12055-024-01842-2","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2024/10/25 0:00:00","PubModel":"Epub","JCR":"Q4","JCRName":"CARDIAC & CARDIOVASCULAR SYSTEMS","Score":null,"Total":0}
Polyostotic fibrous dysplasia in an elderly patient involving spine and ribs.
Fibrous dysplasia (FD) is a benign skeletal disorder characterized by the replacement of normal bone with fibro-osseous tissue, which often causes bone expansion and deformities. Polyostotic fibrous dysplasia (PFD), involving multiple bones, is uncommon and rarely affects the spine and ribs, with fewer than 40 reported cases in the literature. We present the case of a 65-year-old male who presented with sudden left-sided back pain and left sided ptosis. Imaging revealed extensive FD affecting the cervicothoracic vertebrae and the adjacent ribs. Surgical resection involving thoracotomy and excision of the pathological ribs and spinal lesions was performed. The procedure ensured the preservation of vital structures and achieved complete tumor removal. Surgical resection remains crucial in managing symptomatic PFD of the spine and ribs with the aim of complete tumor removal. Long-term follow-up is essential to monitor recurrence and evaluate patient outcomes.
期刊介绍:
The primary aim of the Indian Journal of Thoracic and Cardiovascular Surgery is education. The journal aims to dissipate current clinical practices and developments in the area of cardiovascular and thoracic surgery. This includes information on cardiovascular epidemiology, aetiopathogenesis, clinical manifestation etc. The journal accepts manuscripts from cardiovascular anaesthesia, cardiothoracic and vascular nursing and technology development and new/innovative products.The journal is the official publication of the Indian Association of Cardiovascular and Thoracic Surgeons which has a membership of over 1000 at present.DescriptionThe journal is the official organ of the Indian Association of Cardiovascular-Thoracic Surgeons. It was started in 1982 by Dr. Solomon Victor and ws being published twice a year up to 1996. From 2000 the editorial office moved to Delhi. From 2001 the journal was extended to quarterly and subsequently four issues annually have been printed out at time and regularly without fail. The journal receives manuscripts from members and non-members and cardiovascular surgeons. The manuscripts are peer reviewed by at least two or sometimes three or four reviewers who are on the panel. The manuscript process is now completely online. Funding the journal comes partially from the organization and from revenue generated by subscription and advertisement.