Diagnosis and Management of Natal Tooth Secondary to Beckwith-Wiedemann Syndrome in a 25-day-old Infant: A Rare Case Report.

Beckwith-Wiedemann syndrome (BWS) is a rare genetic disorder characterized by somatic overgrowth and an increased predisposition to various medical conditions, including neoplasms. This case report presents a 25-day-old male infant with BWS exhibiting macroglossia, hepatosplenomegaly, hyperinsulinemic hypoglycemia, gum hypertrophy, and cystic lesions in the maxillary arch, prompting a multidisciplinary collaboration of a pediatrician, pedodontist, oral surgeon, and an oral pathologist. The patient also presented with Hebling's Class III natal tooth. Following all the precautions, the natal tooth was extracted under local anesthesia. This case report stands out for documenting the presence of a natal tooth in a diagnosed case of BWS for the first time, contributing to the understanding of oral manifestations in rare genetic syndromes and underscoring the need for timely intervention and comprehensive medical care in managing this complex genetic syndrome.