遗传性α -胰蛋白酶血症和推定嗜酸性肉芽肿病合并多血管炎1例

The journal of allergy and clinical immunology. Global Pub Date : 2025-04-22 DOI:10.1016/j.jacig.2025.100481

Sonia Iqbal DO , Joseph A. Baxter DO , Karla E. Adams MD

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引用次数: 0

摘要

该病例值得注意的是遗传性α -胰蛋白酶血症和嗜酸性肉芽肿病合并多血管炎的潜在重叠。mepolizumab的成功使用，最初用于嗜酸性肉芽肿病合并多血管炎，但潜在地有益于患者的遗传性α -胰蛋白酶血症，为管理涉及两种罕见疾病的复杂病例提供了一种新的方法。

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A case of hereditary alpha tryptasemia and presumptive eosinophilic granulomatosis with polyangiitis

This case is notable for the potential overlap of hereditary alpha tryptasemia and eosinophilic granulomatosis with polyangiitis. The successful use of mepolizumab, initially for eosinophilic granulomatosis with polyangiitis but potentially benefiting the patient's hereditary alpha tryptasemia, offers a novel approach to managing complex cases involving both rare disorders.

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来源期刊

The journal of allergy and clinical immunology. Global Immunology, Allergology and Rheumatology

CiteScore

0.70

自引率

0.00%

发文量

审稿时长

92 days