更广泛的视角:中低收入国家镰状细胞病患者输血支持的障碍和建议。

IF 5.1 2区 医学 Q1 HEMATOLOGY
Jeremy W Jacobs, Luiz Amorim, France Pirenne, Claude Tayou, Ijele Adimora, Lydia H Pecker, Aaron A R Tobian, Jeannie Callum, Julie Makani, Mark T Gladwin, Meghan Delaney, Darrell J Triulzi, Isaac Odame, Evan M Bloch
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引用次数: 0

摘要

全球范围内,镰状细胞病(SCD)是最常见的遗传性血红蛋白病。慢性阻塞性肺病负担最重的是低收入和中等收入国家(LMICs),其中大多数国家缺乏应对该疾病的资源。高收入国家(HICs)与中低收入国家(LMICs)对SCD患者的护理存在明显差异,只有高收入国家的患者才能获得少数改善疾病的疗法和治疗方案。因此,输血仍然是紧急治疗和预防SCD并发症的核心。然而,在中低收入国家中存在着无数相关的挑战,这些挑战阻碍了有效治疗SCD患者的努力。除了血液安全和可用性,影响SCD的例子还包括检测和/或管理红细胞异体免疫的能力、自动红细胞交换的能力、有限的免疫血液学、不理想的质量监督,缺乏预防输血不相容血液的保障措施,以及输血后检测和/或管理输血相关不良事件的监测有限或缺失。因此,在高收入国家中被视为标准护理的临床实践在中低收入国家中仍然是例外,突出了护理方面的差异。需要采取多方面的方法,优先考虑中低收入国家的输血支持,以改善对SCD患者的护理。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
The wider perspective: Barriers and recommendations for transfusion support for patients with sickle cell disease in low- and middle-income countries.

Globally, sickle cell disease (SCD) is the most common inherited haemoglobinopathy. The highest burden of SCD is encountered in low- and middle-income countries (LMICs), most of which lack the resources to contend with the disease. There is a marked divide between care for individuals with SCD in high-income countries (HICs) versus LMICs, whereby the few disease-modifying therapies and curative regimens are only accessible to those in HICs. As such, blood transfusion remains central to the emergent treatment and prevention of complications of SCD. However, there are a myriad of related challenges in LMICs, which have impeded efforts to treat patients with SCD effectively. In addition to blood safety and availability, examples that impact SCD specifically include capabilities to detect and/or manage red blood cell alloimmunization, capacity for automated red cell exchange, limited immunohematology, suboptimal quality oversight with a lack of safeguards to prevent transfusion of incompatible blood and limited or absent post-transfusion surveillance to detect and/or manage transfusion-associated adverse events. Consequently, clinical practices that are otherwise regarded as standard of care in HICs remain the exception in LMICs, highlighting disparities in care. A multifaceted approach that prioritizes transfusion support in LMICs is needed to improve care for patients with SCD.

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来源期刊
CiteScore
8.60
自引率
4.60%
发文量
565
审稿时长
1 months
期刊介绍: The British Journal of Haematology publishes original research papers in clinical, laboratory and experimental haematology. The Journal also features annotations, reviews, short reports, images in haematology and Letters to the Editor.
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