{"title":"纤维肌肉发育不良引起的快速扩张梭状腹主动脉瘤无狭窄病变一例。","authors":"Shinya Masuda, Daichi Takahashi, Kazuaki Yanagiya, Masayuki Otani, Ko Sakatsume, Nobuaki Suzuki, Ichiro Yoshioka, Masaharu Hatakeyama, Hidekachi Kurotaki, Koichi Nagaya","doi":"10.3400/avd.cr.24-00110","DOIUrl":null,"url":null,"abstract":"<p><p>Fibromuscular dysplasia (FMD) is an arterial disease characterized by fibrous arterial wall thickening and irregular proliferation and degeneration of smooth muscle cells in muscular arteries. Abdominal aortic aneurysms (AAA) are rare, with only a few reported cases. A characteristic feature of AAA is an aneurysm protruding forward near the terminal aorta with stenosis. Here, we report a rare case of a 66-year-old woman who underwent abdominal aortic replacement for a fusiform AAA, diagnosed with aortic FMD (without stenotic lesions) on pathological examination.</p>","PeriodicalId":7995,"journal":{"name":"Annals of vascular diseases","volume":"17 4","pages":"443-446"},"PeriodicalIF":0.6000,"publicationDate":"2024-12-25","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11669020/pdf/","citationCount":"0","resultStr":"{\"title\":\"Rapidly Expanding Fusiform Abdominal Aortic Aneurysm without Stenotic Lesion Caused by Fibromuscular Dysplasia: A Rare Case.\",\"authors\":\"Shinya Masuda, Daichi Takahashi, Kazuaki Yanagiya, Masayuki Otani, Ko Sakatsume, Nobuaki Suzuki, Ichiro Yoshioka, Masaharu Hatakeyama, Hidekachi Kurotaki, Koichi Nagaya\",\"doi\":\"10.3400/avd.cr.24-00110\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>Fibromuscular dysplasia (FMD) is an arterial disease characterized by fibrous arterial wall thickening and irregular proliferation and degeneration of smooth muscle cells in muscular arteries. Abdominal aortic aneurysms (AAA) are rare, with only a few reported cases. A characteristic feature of AAA is an aneurysm protruding forward near the terminal aorta with stenosis. Here, we report a rare case of a 66-year-old woman who underwent abdominal aortic replacement for a fusiform AAA, diagnosed with aortic FMD (without stenotic lesions) on pathological examination.</p>\",\"PeriodicalId\":7995,\"journal\":{\"name\":\"Annals of vascular diseases\",\"volume\":\"17 4\",\"pages\":\"443-446\"},\"PeriodicalIF\":0.6000,\"publicationDate\":\"2024-12-25\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11669020/pdf/\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Annals of vascular diseases\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.3400/avd.cr.24-00110\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"2024/11/27 0:00:00\",\"PubModel\":\"Epub\",\"JCR\":\"Q4\",\"JCRName\":\"PERIPHERAL VASCULAR DISEASE\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Annals of vascular diseases","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.3400/avd.cr.24-00110","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2024/11/27 0:00:00","PubModel":"Epub","JCR":"Q4","JCRName":"PERIPHERAL VASCULAR DISEASE","Score":null,"Total":0}
Rapidly Expanding Fusiform Abdominal Aortic Aneurysm without Stenotic Lesion Caused by Fibromuscular Dysplasia: A Rare Case.
Fibromuscular dysplasia (FMD) is an arterial disease characterized by fibrous arterial wall thickening and irregular proliferation and degeneration of smooth muscle cells in muscular arteries. Abdominal aortic aneurysms (AAA) are rare, with only a few reported cases. A characteristic feature of AAA is an aneurysm protruding forward near the terminal aorta with stenosis. Here, we report a rare case of a 66-year-old woman who underwent abdominal aortic replacement for a fusiform AAA, diagnosed with aortic FMD (without stenotic lesions) on pathological examination.