重型地中海贫血症患者的黏菌血症：一例鼻眶粘孢子菌病

Pediatric Hematology Oncology Journal Pub Date : 2024-09-10 DOI:10.1016/j.phoj.2024.09.003

Dhaarani Jayaraman , Harshavardhan Mahalingam , Naga Geetha Rani Mangam , Swati Narasimhan , Padmasani Venkat Ramanan , K. Stephen Sudhakar , Prasanna Kumar S , Banu Keerthana , Manu Vidhya Harikumar , Anupama Jyoti Kindo , T.K. Shruthi , Niranjan Ragavan , Julius Xavier Scott

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引用次数: 0

摘要

粘孢子菌病是一种可怕的疾病，免疫力低下的宿主死亡率很高。虽然铁超载是一个已知的危险因素，但输血依赖型地中海贫血症患儿患侵袭性粘孢子菌病的报道却很少。我们为您介绍一名患有输血依赖性地中海贫血、脾功能亢进和铁超载的 8 岁女孩。她患有侵袭性菱形眶粘液瘤病，虽然经过积极的手术和药物治疗，但最终还是死亡。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Mucor thriving on iron in beta thalassemia major: A case of rhino-orbital mucormycosis

Mucormycosis is a dreaded condition with high mortality rates noted in immunocompromised hosts. Though iron overload is a known risk factor, children with transfusion-dependent thalassemia have been rarely reported with invasive mucormycosis. We present an 8-year-old girl with transfusion-dependent thalassemia with hypersplenism and iron overload. She had invasive rhino-sino-orbital mucormycosis with a fatal outcome despite aggressive surgical and medical management.

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来源期刊

Pediatric Hematology Oncology Journal

CiteScore

1.00

自引率

0.00%

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