Surgical aortic root replacement in a patient with midaortic syndrome

Background

Midaortic syndrome is a rare condition characterized by the narrowing of the abdominal aorta. In this article, we present a 32-year-old male patient who was incidentally diagnosed with midaortic syndrome, and whose severe aortic regurgitation and ascending aortic dilatation were successfully treated with the Bentall procedure.

Case report

A 32‐year‐old, male patient was admitted to the emergency department with the complaint of chest pain and dyspnea for 3 months. His medical history was notable for diabetes, hypertension (12 years), and hyperthyroidism. Coronary angiography was normal. Ascending aortic dilatation and interrupted abdominal aorta were revealed with computed tomographic angiography (CTA). The Bentall procedure was performed with median sternotomy.

Conclusion

Our case is the first patient in the literature who had Midaortic Syndrome and underwent the Bentall procedure. Additionally, our patient had extremely poor left ventricular functions (LVEF = 20 %). One of the important problems that could occur in this patient was the need for an intra-aortic balloon pump (IABP) for CPB weaning.