Primordial odontogenic tumor of the maxilla: A case report

A primordial odontogenic tumor (POT) consists of an ellipsoidal mass of dental papilla-like myxoid connective tissue entirely enveloped in an intricate membrane of the ameloblastic epithelium. This case has been particularly interesting due to its unique identity and rare nature. A 5-year-old boy came to the ENT department of a tertiary care hospital complaining of left facial swelling for the past three months. In contrast with clinical, radiological, and histological investigations and following the WHO definition, it was confirmed as a Primordial odontogenic tumor of the maxilla. The ideology and genetic makeup of this disease are still idiopathic and in the early developing phase. The clinical, radiologic, microscopic, and IHC features in this case suggest POT in an infrequent location of the anterior maxillary region.