Faraz Yousefian, Mary Michael, Sujitha Yadlapati, Emily Sedaghat, Brad Glick
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引用次数: 0
摘要
复发性多软骨炎(RP)是一种罕见的自身免疫性疾病,炎症反复发作,主要影响软骨和全身其他组织,包括富含蛋白多糖的结构。其特点是组织逐渐变形,导致正常功能受损。涉及的部位包括但不限于呼吸道、眼睛、鼻子、关节和血管系统。炎症主要针对软骨,最常见的是耳软骨炎和鼻软骨炎,但也可累及全身软骨。由于这种全身性疾病的相关症状种类繁多,且症状表现不明显,因此 RP 的诊断往往受到阻碍。在本文中,我们展示了一例伪装成假淋巴瘤的复发性多软骨炎病例,并回顾了与发病机制、诊断和治疗相关的最新文献。
Relapsing Polychondritis Masquerading as Auricular Pseudolymphoma: Case Report and Literature Review
Relapsing Polychondritis (RP) is a rare autoimmune disease associated with recurring inflammatory episodes predominantly affecting cartilage and other tissues throughout the body, including proteoglycan-rich structures. It is characterized by gradual deformation of tissue that leads to impairment of normal function. Areas involved include, but are not limited to, the respiratory tract, eyes, nose, joints, and vascular system. The inflammation targets cartilage, most commonly causing auricular and nasal chondritis but can involve cartilage throughout the body. Diagnosis of RP is often hindered by the vast variety of symptoms associated with this systemic disease and subtle symptomatology. In this paper, we demonstrate a case of relapsing polychondritis masquerading as pseudolymphoma and review recent literature relating to pathogenesis, diagnosis and treatment.