Jennie An, Preye Amaruntowa, Waleed Ahmed, Ali Khan, Muhammad Shahzad
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引用次数: 0
摘要
埃文斯综合征(ES)是一种病因不明的罕见自身免疫性疾病,发生在一小部分先后或同时被诊断为免疫性血小板减少症(ITP)或温性自身免疫性溶血性贫血(AIHA)的患者身上。偶尔会出现中性粒细胞减少。诊断以排除法为基础,中位年龄为 52 岁。这里有一例年轻的 ES 患者,表现为反复感染。对于出现 AIHA、ITP、细胞减少症或反复感染的患者,应将 ES 列入鉴别诊断,因为在早期诊断且症状尚轻时,预后更佳。
Recurrent Infection in a Young Female Patient Recently Diagnosed With Primary Evans Syndrome Without Neutropenia.
Evans syndrome (ES) is a rare autoimmune condition of unknown etiology that occurs in a small subset of patients diagnosed, either sequentially or concomitantly, with immune thrombocytopenia (ITP) or warm autoimmune hemolytic anemia (AIHA). Neutropenia is present occasionally. Diagnosis is based on exclusion with a median age of 52 years of age. Here we have a case of a young patient with ES presenting with recurrent infection. ES should be included in differential diagnoses for patients presenting with AIHA, ITP, cytopenias or recurrent infection as the prognosis is more favorable when diagnosis is made early and symptoms are still mild.