脾脏和骨骼的上皮样血管内皮瘤：病例报告。

IF 1 4区医学 Q4 RADIOLOGY, NUCLEAR MEDICINE & MEDICAL IMAGING

Journal of the Belgian Society of Radiology Pub Date : 2024-06-25 eCollection Date: 2024-01-01 DOI:10.5334/jbsr.3600

Melvin Denolf, Annelies Rappaport, Sigrun Delvaux

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引用次数: 0

摘要

上皮样血管内皮瘤（EHE）是一种罕见的血管肿瘤，可起源于各种实质性器官、软组织和骨骼。肝外受累极为罕见。在该病例中，脾脏和骨骼出现多灶性病变。骨病变呈靶状。脾脏病变显示实性成分延迟强化，边缘持续强化。经CAMTA1染色的骨活检确诊。教学要点在排除其他多灶性疾病的情况下，出现多灶性骨和脾病变可引起对 EHE 的怀疑。

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Epithelioid Hemangioendothelioma of Spleen and Bone: A Case Report.

Epithelioid hemangioendothelioma (EHE) is a rare vascular tumor that can originate in various parenchymatous organs, soft tissue, and bone. Extrahepatic involvement is exceedingly rare. In this case, multifocal disease in the spleen and bone was present. Bone lesions showed a target appearance. Splenic lesions showed delayed enhancement of solid components with persistent rim enhancement. A bone biopsy with CAMTA1 staining confirmed the diagnosis. Teaching point: The presence of multifocal bone and splenic lesions can raise suspicion of EHE when other multifocal diseases are excluded.

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来源期刊

Journal of the Belgian Society of Radiology Medicine-Radiology, Nuclear Medicine and Imaging

CiteScore

0.70

自引率

5.00%

发文量

期刊介绍： The purpose of the Journal of the Belgian Society of Radiology is the publication of articles dealing with diagnostic and interventional radiology, related imaging techniques, allied sciences, and continuing education.