镰状细胞病患儿脂肪栓塞综合征--一种诊断不足的病症：病例报告

Pediatric Hematology Oncology Journal Pub Date : 2024-06-13 DOI:10.1016/j.phoj.2024.06.001

Sohini Chakraborty , Arun Danewa , Sunisha Arora , Saurabh Bansal , Parminder Pal Singh , Rahul Bhargava , Vikas Dua

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引用次数: 0

摘要

背景脂肪栓塞综合征（FES）是镰状细胞病的一种罕见且诊断不足的并发症。病例报告我们报告了一例 12 岁镰状细胞病女孩的病例，她最初表现为急性血管闭塞危象。然而，她后来出现了神经系统和呼吸系统并发症，同时血红蛋白和血小板计数下降。经过评估，她被诊断为 FES。结论及时诊断和早期治疗可以显著改善这种罕见但发病率很高的并发症的预后。

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Fat embolism syndrome in a child with sickle cell disease

Background

Fat embolism syndrome (FES) is a rare and underdiagnosed complication associated with sickle cell disease.

Case report

We report the case of a 12-year-old girl with sickle cell disease who initially presented with features of acute vaso-occlusive crisis. However, she later developed neurological and respiratory complications along with a decrease in hemoglobin and platelet counts. She was evaluated and diagnosed with FES. The patient was successfully managed with red cell exchange and therapeutic plasma exchange, leading to complete recovery.

Conclusion

Prompt diagnosis and early management can significantly improve the outcome of this rare, though highly morbid complication.

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来源期刊

Pediatric Hematology Oncology Journal

CiteScore

1.00

自引率

0.00%

发文量