[特发性炎症性肌病:跨学科挑战]。

IF 0.9 4区 医学 Q4 RHEUMATOLOGY
Zeitschrift fur Rheumatologie Pub Date : 2024-08-01 Epub Date: 2024-06-12 DOI:10.1007/s00393-024-01523-w
Dana Lemmer, Tobias Ruck, Anne Schänzer, Konstantinos Triantafyllias, Rachel Zeng, Rebecca Hasseli-Fräbel
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引用次数: 0

摘要

特发性炎症性肌病(IIM)是一种罕见疾病(发病率为 1:100,000),临床症状和表现多种多样。特发性炎症性肌病的典型症状是近端强调性肌无力和肌痛,通常伴有肌酸激酶水平升高和肌肉萎缩。自身抗体诊断将 IIM 分成不同的实体,每个实体都与典型的器官表现和肿瘤发生风险相关。IIM 是一项跨学科挑战,诊断和治疗需要多个学科的参与,包括风湿病学、神经病学、神经病理学、皮肤病学和肺病学。准确的诊断和仔细的肿瘤筛查至关重要,因为某些 IIM 亚群与恶性肿瘤的发生存在关联。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
[Idiopathic inflammatory myopathies : An interdisciplinary challenge].

Idiopathic inflammatory myopathies (IIM) are rare diseases (incidence 1:100,000) with a wide range of clinical symptoms and manifestations. Typical indicators of IIM are proximally emphasized muscle weakness and myalgias, which are usually accompanied by elevated creatine kinase levels and muscle atrophy. The autoantibody diagnostics separate IIM into different entities, which are each associated with a typical risk of organ manifestations and the occurrence of tumors. The IIM represents an interdisciplinary challenge and the diagnostics and treatment require the involvement of several disciplines including rheumatology, neurology, neuropathology, dermatology and pneumology. An accurate diagnosis and careful tumor screening are essential because of the association between certain subgroups of IIM and the occurrence of malignant tumors.

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来源期刊
Zeitschrift fur Rheumatologie
Zeitschrift fur Rheumatologie 医学-风湿病学
CiteScore
2.20
自引率
20.00%
发文量
150
审稿时长
6-12 weeks
期刊介绍: Die Zeitschrift für Rheumatologie ist ein international angesehenes Publikationsorgan und dient der Fortbildung von niedergelassenen und in der Klinik tätigen Rheumatologen. Die Zeitschrift widmet sich allen Aspekten der klinischen Rheumatologie, der Therapie rheumatischer Erkrankungen sowie der rheumatologischen Grundlagenforschung. Umfassende Übersichtsarbeiten zu einem aktuellen Schwerpunktthema sind das Kernstück jeder Ausgabe. Im Mittelpunkt steht dabei gesichertes Wissen zu Diagnostik und Therapie mit hoher Relevanz für die tägliche Arbeit – der Leser erhält konkrete Handlungsempfehlungen. Frei eingereichte Originalien ermöglichen die Präsentation wichtiger klinischer Studien und dienen dem wissenschaftlichen Austausch.
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