Swyer - James - 一名成年男性的麦克劳德综合征

Q4 Medicine
A. М. Makarevich, A. Zaytsev, E. М. Makarevich
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引用次数: 0

摘要

斯怀尔-詹姆斯综合征(Swyer-James Syndrome),又称斯怀尔-詹姆斯-麦克劳德综合征(Swyer-James-MacLeod Syndrome,SJMS),是一种罕见的获得性疾病,以肺动脉发育不良、单侧肺过度透明为特征,通常还伴有支气管扩张。由于临床表现相似,成人 SJMS 患者通常被诊断为慢性阻塞性肺病 (COPD)、支气管哮喘、气胸或肺栓塞,并接受相关治疗。由于低估了一个重要的放射学征象--单侧 "贫困化 "的肺部形态和高透明肺--导致诊断错误和治疗不当。诊断 SJMS 需要进行胸部计算机断层扫描。本文旨在让读者熟悉诊断的各个方面,并详细介绍一名麦克劳德综合征患者的临床、放射学和其他特征。所描述的成年男子在 32 岁时被诊断出患有 SJMS。文中介绍了此类患者检查中的一些典型错误,以及放射科医生对单侧高透明肺缺乏警惕的情况。结论。我们以一个罕见的 SJMS 临床病例为例,说明在诊断无故气短、有频繁复发肺部感染病史、放射学表现为单侧肺气肿和肺透明层增高的成人时,有必要考虑到这一综合征。根据文献和我们的观察,胸部器官计算机断层扫描是确诊 SJMS 的一种快速、可靠的方法。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Swyer – James – McLeod syndrome in an adult male
Swyer – James syndrome, also called Swyer – James – MacLeod syndrome (SJMS), is a rare acquired disorder characterized by pulmonary artery hypoplasia, unilateral hyperlucent lungs, and usually also bronchiectasis. Adults with SJMS are often diagnosed with and treated for chronic obstructive pulmonary disease (COPD), bronchial asthma, pneumothorax, or pulmonary embolism due to the similar clinical manifestations. Underestimation of an important radiological sign – unilateral “impoverishment” of the pulmonary pattern and hyperlucent lung – leads to erroneous diagnosis and inadequate treatment. Diagnosis of SJMS involves a computed tomography scan of the chest. The aim of this work was to familiarize readers with aspects of diagnosis and detail the clinical, radiological, and other characteristics of a patient with McLeod syndrome. The described adult man was diagnosed with SJMS at the age of 32. Some typical mistakes in examinations of such patients and the lack of vigilance of radiologists in case of unilateral hyperlucent lung are presented. Conclusion. Using the example of a rare clinical case of SJMS, we demonstrated the need to consider this syndrome when diagnosing adults with unjustified shortness of breath and a history of frequently recurrent pulmonary infections, with radiological signs of unilateral pulmonary emphysema and hyperlucent lung. According to the literature and our observations, computed tomography of the chest organs is a fast and reliable method for establishing the diagnosis of SJMS.
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来源期刊
Pulmonologiya
Pulmonologiya Medicine-Pulmonary and Respiratory Medicine
CiteScore
1.40
自引率
0.00%
发文量
70
期刊介绍: The aim of this journal is to state a scientific position of the Russian Respiratory Society (RRS) on diagnosis and treatment of respiratory diseases based on recent evidence-based clinical trial publications and international consensuses. The most important tasks of the journal are: -improvement proficiency qualifications of respiratory specialists; -education in pulmonology; -prompt publication of original studies on diagnosis and treatment of respiratory diseases; -sharing clinical experience and information about pulmonology service organization in different regions of Russia; -information on current protocols, standards and recommendations of international respiratory societies; -discussion and consequent publication Russian consensus documents and announcement of RRS activities; -publication and comments of regulatory documents of Russian Ministry of Health; -historical review of Russian pulmonology development. The scientific concept of the journal includes publication of current evidence-based studies on respiratory medicine and their discussion with the participation of Russian and foreign experts and development of national consensus documents on respiratory medicine. Russian and foreign respiratory specialists including pneumologists, TB specialists, thoracic surgeons, allergists, clinical immunologists, pediatricians, oncologists, physiologists, and therapeutists are invited to publish article in the journal.
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