贾乔-列文综合征伴开放性神经管缺陷:病例报告

Q4 Medicine
Md Mokarram Ali, Y. Kadian, Saima Ejaz, A. Kadian
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引用次数: 0

摘要

背景介绍贾乔-莱文综合征是一种罕见的遗传性疾病,以脊柱畸形和无肋骨为特征。它伴有各种先天性畸形,发病率和死亡率都很高。同时伴有神经管缺陷的病例很少见:我们报告了一例出生仅 2 天的男性病例。临床和放射学检查显示,患者胸腰椎脑膜疝,右侧上肋骨缺失,卵圆孔通畅。随后,患者接受了脑膜疝手术,而肋骨异常则采取了保守治疗:结论:贾尔乔-莱文综合征是一种罕见疾病,与脑膜瘤相关的病例极为罕见。结论:贾尔乔-莱文综合征是一种罕见疾病,与脑膜瘤相关的病例极为罕见,在评估有神经管缺陷和呼吸窘迫的患者时应考虑到这种疾病。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Jarcho Levin Syndrome with open neural tube defect: A case report
Background: Jarcho Levin syndrome is a rare genetic disorder characterized by spine abnormalities and the absence of ribs. It is associated with various congenital malformations and carries significant morbidity and mortality. The simultaneous presentation of this syndrome with neural tube defects is seldom encountered. Case Presentation: We report a case of a 2-day-old male who presented with a lesion on his back since birth. Clinical and radiological examinations revealed thoracolumbar meningomyelocele with the absence of upper ribs on the right side and a patent foramen ovale. Subsequently, the patient underwent surgery for meningomyelocele, while the rib anomalies were managed conservatively. Conclusion: Jarcho Levin syndrome is a rare disorder, and its association with meningomyelocele is extremely uncommon. It should be considered in the evaluation of a patient with a neural tube defect and respiratory distress.
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来源期刊
Journal of Neonatal Surgery
Journal of Neonatal Surgery Medicine-Surgery
CiteScore
0.30
自引率
0.00%
发文量
29
审稿时长
6 weeks
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