单侧开角型青光眼并发桡骨毛面综合征的罕见病例

Rakesh Shakya, N. Ahluwalia, R. P. Maurya, Chintan Shah, Nidhi Gupta, B. K. Jain
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引用次数: 0

摘要

巩膜外静脉压升高(EEVP)是眼内压升高的一个罕见但重要的原因。由此导致的青光眼往往很严重,常规抗青光眼治疗也难以奏效。它通常是由于动静脉瘘或静脉充血引起的。发现这种病症非常重要,因为它可能与球后肿瘤、海绵窦血栓、纵隔肿瘤等严重病症有关。在排除这些疾病后,EEVP 被认为是特发性的。在这里,我们描述了特发性 EEVP(又称 Radius-Maumenee 综合征)以及详细的诊断和治疗方法。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
A rare case of Radius Maumenee syndrome with unilateral open angle glaucoma
Elevated episcleral venous pressure (EEVP) is a rare but important cause of raised intraocular pressure. The resultant glaucoma is often severe and refractory to routine anti glaucoma treatment. Usually it occurs due to arteriovenous fistulas or venous congestion. This entity is important to detect as it may be associated with serious pathologies like retrobulbar tumor, cavernous sinus thrombosis, mediastinal tumor to name a few. EEVP is considered idiopathic after ruling out such disorders. Here, we have described idiopathic EEVP also known as Radius-Maumenee syndrome along with a detailed diagnostic and therapeutic approach of management.
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